静脉畸形骨肥大综合征的诊治  

The diagnosis and treatment of Klippel-Trenaunay syndrome

作　　者：闫波[1] 苏少飞[1] 田玉峰[1] 

机构地区：[1]宁夏医科大学第二附属医院血管外科,银川75000

出　　处：《中国血管外科杂志（电子版）》2013年第2期103-105,共3页Chinese Journal of Vascular Surgery(Electronic Version)

摘　　要：目的探讨静脉畸形骨肥大综合征(KTS)的诊治方法及预后。方法对1997年1月～2012年1月治疗的21例KTS患者的临床资料进行回顾性分析,根据患者不同的临床表现、术前血管造影、CT及磁共振成像检查结果选择不同治疗方案。结果 5例保守治疗(穿厚底鞋)患者中4例症状(肢体增长)得到改善,1例未坚持穿厚底鞋患者的症状加重;硬化剂注射治疗(3例)、栓塞治疗(3例)、单纯血管瘤(痣)样组织切除(3例)和血管瘤切除+剥脱曲张浅静脉+膝下动静脉交通支切断(6例)及行管状动-静脉瘘切除结扎(1例)的患者,在随访期(随访时间1~9年,平均随访51个月)症状获得改善并得到控制13例,2例在术后3年血管瘤(痣)复发。结论 KTS经正确选择治疗方案并进行处理后,大部分患者的临床症状可以改善并得到控制。Objective To investigate diagnosis, treatment and prognosis of Klippel-Trenaunay syndrome(KTS). Method From Jan.1997 to Jan.2012, the clinical data of 21 patients with KTS were analyzed retrospectively. On the basis of clinical symptoms, computed tomography angiography and magnetic resonance imaging, 21 patients were diagnosed. Result Five patients were treated by special shoe-pad, 3 patients by sclerotherapy, 3 patients by cavernouscotomy simply. Six patients with arteriovenous fistula were treated by ligation of arteriovenous fistula and outsidevascular isolation with graft. Other cases with tubal arteriovenous fistula by ligation of fistula. Follow-up time 1 to 9 years, average 51 months. the symptoms of 17 patients have improved, 2 cases recurred, 1 case get worse. Conclusion Dreessing special shoe-pad early and cutting off arteriovenous fistula are effictive to treat the Klippel-Trenaunay syndrome.

关 键 词：静脉畸形骨肥大综合征 硬化剂治疗 栓塞治疗 

分 类 号：R654.3[医药卫生—外科学]