Superior mesenteric artery syndrome in a patient with Charcot Marie Tooth disease  

作　　者：óscar Dario Gómez Beltrán Amparo Valverde Martínez María del Carmen Pérez Manrique Joaquín Sánchez Rodríguez Enrique Lizárraga Febres Sebastián Ruf ián Pea 

机构地区：[1]Department of General Surgery,Reina Sofía Teaching Hospital

出　　处：《World Journal of Gastrointestinal Surgery》2011年第12期197-200,共4页世界胃肠外科杂志（英文版）（电子版）

摘　　要：The extrinsic compression of the third part of the duodenum as it passes through the aorto-mesenteric angle is known as the superior mesenteric artery syndrome(SMAS).This syndrome is a rare mechanical cause of upper intestinal obstruction,with a reported incidence of between 0.2% and 0.78%.Clinical manifestations of SMAS may be chronic or acute;chronic symptoms include intermittent gastric pain,fullness and occasional episodes of postprandial vomiting,while acute symptoms include incoercible vomiting,oral intolerance,mainly epigastric abdominal distension and abdominal pain.Surgery is recommended only when initial conservative treatment fails.Here,we report what appears to be the third published case of SMAS associated with hereditary motor and sensory neuropathy or Charcot Marie Tooth disease.The extrinsic compression of the third part of the duodenum as it passes through the aorto-mesenteric angle is known as the superior mesenteric artery syndrome (SMAS). This syndrome is a rare mechanical cause of upper intestinal obstruction, with a reported incidence of between 0.2% and 0.78%. Clinical manifestations of SMAS may be chronic or acute; chronic symptoms include intermittent gastric pain, fullness and occasional episodes of postprandial vomiting, while acute symptoms include incoercible vomiting, oral intolerance, mainly epigastric abdominal distension and abdominal pain. Surgery is recommended only when initial conservative treatment fails. Here, we report what appears to be the third published case of SMAS associated with hereditary motor and sensory neuropathy or Charcot Marie Tooth disease.

关 键 词：Superior mesenteric artery Wilkie´ s syndrome Aorto-mesenteric distance DUODENOJEJUNOSTOMY Hereditary neuropathy 

分 类 号：R657.2[医药卫生—外科学]