结节性硬化的CT诊断价值  

CT Dignosis Evalue of Tuberous Sclerosis

作　　者：张增俊[1] 黄明侠[1] 谌天华[1] 刘勃[1] 曹玉琴[1] 杜毛绳[1] 

机构地区：[1]西安市儿童医院CT室,z710002

出　　处：《中国医学影像学杂志》2005年第1期1-2,共2页Chinese Journal of Medical Imaging

摘　　要：目的 :研究结节性硬化的CT特点及其诊断价值。材料和方法 :回顾性研究 3 1例结节性硬化的CT表现。结果 :临床上面部病变、癫痫和智力障碍三联征 15例 ,占 48.4%。CT表现 :室管膜下结节 ,钙化 18例 ,未钙化 3例 ,位于双侧侧脑室前角 13例 ,体部 6例和颞角 2例以及Ⅳ脑室 1例。皮质结节 6例和白质异常 3例以及近孟氏孔巨细胞星形细胞瘤致阻塞性脑积水 1例。结论 :室管膜下 /皮质钙化 /未钙化结节是非常重要的CT诊断结节性硬化的征象 ,结合临床三联征能准确诊断。Purpose: To study CT characteristics and diagnostic evaluation of Tuberous sclerosis. Materials and Methods: The CT features in 31 patients with tuberous sclerosis were studied retrospectively. Results: The clinic triad of popular facial lesions,seizures and mental retardation was seen in 15 cases(48.4%).CT showed subpendymal tubers(calcified one in 18 cases, non calcified one in 3 cases),located near bilateral frontal horns in 13 cases,bodies in 6 cases,temporal horns in 2 cases,of lateral ventricles, and Ⅳ ventricles in 1 cases.cortical tubers in 6 cases and white matter abnormalities in 3 cases and obstructive hydrocephalus caused by subpendymal gaint cell astrocytoma near the foramen of Monro in one case. Conclusion: subpendymal and/or cortical calcified and/or non-calcified tubers are very important diagnostic CT signs for tuberous sclerosis,when associated with clinic triad,can make a corrective diagnosis.

关 键 词：脑 结节性硬化 CT 诊断 

分 类 号：R816.1[医药卫生—放射医学]