晚发性脊椎骨骺发育不良伴进行性关节病  

Spondyloepiphyseal Dysplasia Tarda with Progressive Arthropathy

作　　者：郭琪[1] 陈志刚[2] 杨广夫[2] 马茂林[2] 钱致中[2] 

机构地区：[1]陕西省人民医院放射科,710068 [2]西安医科大学第一附属医院影像中心

出　　处：《实用放射学杂志》1996年第6期336-338,共3页Journal of Practical Radiology

摘　　要：本文报告3例晚发性脊椎骨骺发育不良伴进行性关节病.临床儿童期出现进行性关节肿痛挛缩,成人后关节肥大畸形,可出现脊髓受压表现.X线特点为椎体普遍变扁,关节肥大退变,骨骺变形碎裂,骨盆发育异常.MR表现椎间盘变性膨出,脊髓受压.Three cases of SEDTPA were reported. The disease presents clinically in mid-childhood as progressive contracture. It presents in adult as features of compression of spinal cord. The X-ray features are generalized platyspondyly, degenerative arthropathy, deformative and brocken epiphyses, and pelvis abnormality. The MR features are degeneration and protrusion of intervertebral disc, and compresson of sinal cord.

关 键 词：骨发育异常 关节病 X线诊断 

分 类 号：R816.8[医药卫生—放射医学] R681.104[医药卫生—临床医学]