Sturge-Weber综合征的CT分析(附13例报告)  

CT analysis of Sturge-Weber syndrome:a report of 13 cases

作　　者：周伟文[1] 何旭升[1] 冯友权[2] 林永文[3] 

机构地区：[1]广东医学院第二附属医院放射科,广东湛江524003 [2]广东医学院附属医院放射科 [3]广东医学院附属医院儿科

出　　处：《实用医学影像杂志》2005年第5期254-256,共3页Journal of Practical Medical Imaging

摘　　要：目的探讨Sturge-Weber综合征的病理变化和CT表现特征。方法收集13例Sturge-Weber综合征的临床和CT资料,所有病例均进行常规螺旋CT扫描。结果在CT像上,13例均见病灶内钙化,其中,轻度钙化4例,中度钙化8例,重度钙化1例;脑萎缩10例,其中,6例受累脑叶灰白质分界不清;脉络丛扩大3例;颅骨增厚6例。结论脑叶皮层“脑回样”钙化是Sturge-Weber综合征的特征性表现,CT是确诊该病的重要检查手段。Objective To investigate the pathologic changes of Stuge - Weber syndrome and its characteristic CT findings. Methods The clinical and CT data of 13 patients with clinically considered Sturge - Weber syndrome were collected and analyzed. All patients underwent conventional spiral CT scans. Results On CT images, gyriform calcification was found in all patients who included 4 slight, 8 midding, and 1 severe calafication. Cerebral atrophy was found in 10 cases, of them, 6 cases presented an unclear demarcation between gray and white matter in affected brain lobes. Choroid plexus enlargement and thickened calvarium were found in 3 and 6 cases, respectively. Conclusion The gyriform calcification in cerebral cortex is a characteristic finding of Sturge - Weber syndrome while CT scanning is the most important means for diagnosing this disease.

关 键 词：STURGE-WEBER综合征 脑萎缩 脑回样钙化 断层摄影术 X线计算机 

分 类 号：R816.1[医药卫生—放射医学]