儿童嗜铬细胞瘤8例报告  

Pheochromocytoma in Children:a report of 8 cases

作　　者：范欣荣[1] 李汉忠[1] 宋宗禄[1] 夏溟[1] 肖河[1] 李永强[1] 曾正陪[2] 

机构地区：[1]中国医学科学院中国协和医科大学北京协和医院泌尿外科,北京100730 [2]中国医学科学院中国协和医科大学北京协和医院内分泌科,北京100730

出　　处：《中国实用外科杂志》2006年第3期204-206,共3页Chinese Journal of Practical Surgery

摘　　要：目的探讨儿童嗜铬细胞瘤的临床特点及诊治方法。方法对1984～2004年诊治的8例儿童嗜铬细胞瘤进行回顾性分析。术前通过临床表现、24h尿儿茶酚胺、131碘间碘苄胍全身核素扫描(131IMIBG扫描)、B超或CT检查明确定性及定位诊断。并用α受体阻滞剂行术前药物准备。结果8例均行手术切除肿瘤;病理诊断:良性5例,恶性3例。结论儿童嗜铬细胞瘤少见,病情进展快;早期诊断、手术切除是目前惟一可治愈的方法。Objective To investigate the clinical features, diagnosis, and treatment of pheoehromocytoma in children. Methods Eight cases of children pheochromocytoma in Peking Union Medical College Hospital from 1984 to 2004 were analyzed retrospectively. Definitive diagnosis and localization of the tumor were made preoperatively by clinical manifesta- tions,24-hour urinary catecholamine,^131I-MIBG, B-ultrasound and CT scan. Preoperative management with α-adrenergic receptor blocker was performed. Results Tumor resection was performed in all 8 patients and the diagnosis was confirmed by pathological results, in which 5 were benign and 3 were malignant. Conclusion Pheochromocytoma is rare in children, and the development is fast. Early diagnosis and surgical excision is the only way to cure the disease.

关 键 词：嗜铬细胞瘤 肾上腺 

分 类 号：R6[医药卫生—外科学]