室间隔缺损病理解剖分类的再认识  被引量:5

Recognition the Pathologic Anatomic Classification of Ventricular Septal Defect

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作  者:陈会文[1] 苏肇伉[1] 丁文祥[1] 徐志伟[1] 刘锦纷[1] 张海波[1] 

机构地区:[1]上海第二医科大学附属新华医院上海儿童医学中心小儿心胸外科,上海200127

出  处:《中国胸心血管外科临床杂志》2006年第2期89-93,共5页Chinese Journal of Clinical Thoracic and Cardiovascular Surgery

摘  要:目的对室间隔缺损(VSD)的病理解剖分类进行再认识和评价。方法选取我院2002年1月至2004年10月单纯室间隔缺损患者119例(≤10kg),术前心脏彩色超声心动图结合术中探查确定室间隔缺损的病理解剖分类。结果(1)膜周室间隔缺损51例(直径0.6±1.0 cm),完全位于膜部的室间隔缺损8例(直径0.5±0.4 cm),偏流入道21例(直径0.8±0.5 cm),偏流出道14例(直径1.0±0.6 cm),偏小梁部8例(直径0.8±0.6 cm);其中有假性室隔瘤形成14例(直径0.5±0.3 cm)。(2)圆锥隔心室型室间隔缺损共21例(直径1.2±0.8 cm),其中周缘全是肌性13例,向膜部延伸8例;隔束肥厚14例,主动脉瓣下狭窄5例。(3)肺动脉瓣下型室间隔缺损26例(直径0.8±0.8 cm),其中近邻肺动脉瓣18例,与肺动脉瓣有肌性相隔8例;单纯位于肺动脉瓣下20例,主动脉瓣和肺动脉瓣下6例。(4)房室通道型或流入道型室间隔缺损10例(直径1.2±0.8 cm)。(5)肌部型室间隔缺损11例(直径0.4±0.3 cm),其中单发性3例,多发性8例。结论将室间隔缺损分为膜周型、圆锥隔心室型、房室通道型、肺动脉瓣下或圆锥隔型和肌部型更具有临床意义。Objective To recognize and reevaluate the pathologic anatomic classification of ventricular septal defect (VSD). Methods From January,2002 to October,2004,119 patients less than 10kg of body weight with simple VSD whose pathologic anatomic classification was determined by preoperative echocardiography and ascertained during surgery were choosed randomly. Results (1) There were fihy-one patients with perimembranous VSD (diameter 0. 6±1.0 cm), 8 VSD situated in the membranous septum (diameter 0. 5±0.4 cm), 21 VSD extending to inlet (diameter 0.8±0.5 cm), 14 extending to outlet (diameter 1.0±0. 6 cm) and 8 extending to trabecula (diameter 0. 8±0.6 cm). In this group, accessory tricuspid valve tissue was formed in 14 patients(diameter 0. 5±0.3 cm). (2) Twenty-one patients had conoventricular VSD (diameter 1.2±0. 8 cm), among them 13 VSD had muscle margins, 8 extending to membranous septum, 14 had septal band hypertrophy, and 5 had subaortic stenosis. (3) Twenty-six patients had subpulmonary VSD(diameter 0.8±0.8 cm), 18 VSD lay immediately below pulmonary valve, 8 had muscle distant from pulmonary valve, 20 lay completely below pulmonary valve, and 6 lay below pulmonary valve and aortic valve. (4) Ten patients were atrioventricular canal type or inlet VSD (diameter 1.2±0.8 cm). (5)Eleven patients had muscular VSD, among them 3 were single ,and 8 multiple (diameter 0. 4±0.3 cm). Conclusion It will be more clinically significant that VSD is classified into perimembranous, conoventricular, atrioventricular canal or inlet, muscular and subpulmonary artery or conical types.

关 键 词:室间隔缺损 病理解剖 分类 

分 类 号:R726.5[医药卫生—儿科]

 

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