先天性单侧肾发育不良合并输尿管异位开口27例报道  

Congenital Renal Single Dysplasia in Association With Ectopic Ureter:A Report of 20 Cases

作　　者：汤凤萍[1] 李爽[1] 王军[1] 杨世友[1] 周辉霞[1] 戴世希[1] 

机构地区：[1]武汉市儿童医院泌尿外科,湖北武汉430016

出　　处：《临床小儿外科杂志》2006年第4期265-267,共3页Journal of Clinical Pediatric Surgery

摘　　要：目的总结先天性单侧肾发育不良合并输尿管异位开口的诊治经验。方法对27例先天性单侧肾发育不良合并输尿管异位开口患儿的临床表现、诊治方法进行回顾性分析。结果27例患儿均为女性。左侧18例,右侧9例。经B超、静脉尿路造影(IVU)、阴道逆行造影、CT、MRI等检查证实,17例输尿管异位开口于阴道壁,3例开口于尿道与阴道口之间。16例发现发育不良的肾脏。27例患儿均接受了发育不良肾及输尿管切除术。结论先天性单侧肾发育不良合并输尿管开口异位通过病史、体格检查及影象学检查,可于术前得到确诊,手术切除发育不良的肾脏及输尿管,疗效满意。Objective To summarize the experience on diagnosis and treatment of congenital renal single dysplasia in association with ectopic ureter. Methods The clinical feature, diagnosis and treatment of 20 cases congenital renal dysplasia with ectopic ureter were retrospectively analysed. Results All the cases were female, 12 cases of all renal dysplasia located in left, 8 cases right. With the examination of B-ultrasound, Transvaginal Color Doppler and CT, 15 cases ectopic ureter were located in the wall of vagina, 3 cases vestibule, 2 cases the wall of urinary duct, which were the same as finds in the operation. 20 cases were undertaken the nephrectomy and ureterectomy, the kidneys volume is small,and abnormal morphology and anomalistic position were seen. After the surgery, symptom of incontinence was disappeared soon. Conclusions Congenital renal dysplasia with ectopic ureter can be diagnosed by history, physical check-up and special examination. The prognosis is good by resectional therapy of dysplasia kidney and ureterectomy.

关 键 词：肾/畸形 输尿管/畸形 

分 类 号：R726.921[医药卫生—儿科]