肺泡蛋白沉积症的影像学特点分析  

Analysis of Radiological Features of Pulmonary Alveolar Proteinosis

作　　者：张大勇[1] 马永强[1] 刘星彤[2] 魏茂泉 

机构地区：[1]北京协和医院放射科,北京100730 [2]吉林省白城市中心医院放射科 [3]吉林省白山市中心医院放射科

出　　处：《实用放射学杂志》2007年第4期461-462,474,共3页Journal of Practical Radiology

摘　　要：目的探讨肺泡蛋白沉着症(PAP)的影像特征及诊断方法。方法对37例经纤维支气管镜活检或开胸活检病理及肺泡灌洗证实的原发性肺泡蛋白沉着症患者的胸片和CT表现进行回顾性分析。结果PAP胸部影像表现呈多样化,可归纳为地图样表现、碎石路样表现、肺实变表现(支气管充气征)以及肺间质纤维化样表现等。肺部阴影重且相对稳定而临床症状较轻,可出现临床症状与影像学表现分离现象。结论肺泡蛋白沉积症具有上述典型的影像学特征,结合临床不难做出正确诊断。Objective To analyse the radiological features and the diagnostic method of pulmonary alveolar proteinosis（ PAP）. Methods X - ray and CT manifestations of PAP in 37 cases confirmed with fiberoptic bronchoscopy and bronchoalveolar lavage were studied retrospectively. Results The radiologic features of PAP could be characterized as geographic, the ＂crazy - paving＂ pattern,lobar or segmental consolidation （ air - brochogram sign） and like intersititial fibrosis. The radiologic manifestations were stable and more serious than the symptoms. Conclusion PAP is of typical radiologic feature,it is not difficult for diagnosis in combination with clinical characteristics.

关 键 词：肺 肺泡蛋白沉着症 X线摄影术 体层摄影术 X线计算机 

分 类 号：R563[医药卫生—呼吸系统] R814.41[医药卫生—内科学]