特发性视网膜血管炎、动脉瘤、视神经视网膜炎综合征临床观察  

Three cases with idiopathic retinal vasculitis, aneurysms, and neuroretinitis syndrome

作　　者：严密[1] 廖菊生[2] 张美霞[1] 韦纯义[1] 唐健[1] 张军军[1] 孟丹[1] 

机构地区：[1]四川大学华西医院眼科,成都610041 [2]河北医科大学第二医院眼科

出　　处：《中华眼底病杂志》2007年第3期180-183,共4页Chinese Journal of Ocular Fundus Diseases

摘　　要：目的观察特发性视网膜血管炎、动脉瘤、视神经视网膜炎综合征（IRVAN综合征）的临床特征。方法回顾分析3例经全身系统检查、眼底彩色照相以及荧光素眼底血管造影（FFA）等检查确诊的IRVAN综合征患者的临床资料。结果3例患者均有特发性视网膜血管炎，而且是视网膜动脉的炎症，视盘及视网膜血管多发性大动脉瘤以及因视盘水肿、视盘周围渗出引起的视神经视网膜炎，2例患者周边部视网膜血管有闭塞区。结论IRVAN综合征的临床特征有特发性视网膜血管炎，视网膜和视盘动脉血管管壁上多发性大动脉瘤，以及由于血管炎症和动脉瘤引起的视网膜、视盘渗出、水肿以及由此产生的视神经视网膜炎。Objective To observe the clinical characteristics of idiopathic retinal vasculitis, aneurysms, and neuroretinitis （IRVAN） syndrome. Methods The clinical data of 3 patients with IRVAN syndrome which were diagnosed by systemic examination, fundus photography and fundus fluorescein angiography （FFA） were retrospectively analyzed. Results Idiopathic retinal vasculitis, which was induced by retinal arterial inflammation, multiple macroaneurysms of optic disc and retinal vessels, edema of optic disc, and exudation around the optic disc, was found in all of the 3 patients, multiple arteriolar aneurysms of optic disc and retinal vascular and exudative neuroretinitis. Two patients had peripheral retinal vascular nonperfusion area, which belonged to typical IRVAN syndrome. Conclusions The clinical characteristics of IRVAN syndrome include idiopathic retinal vasculitis which only involved in artery, multiple retinal macroaneurysms which located on the dissepiment of optic disc and retinal artery, and the neuroretinitis induced by exudation of retina and optic disc because of vasculitis and aneurysms.

关 键 词：视网膜血管炎 视网膜炎 综合征 

分 类 号：R686[医药卫生—骨科学]