小儿多囊肾33例临床分析  

Clinical study of 33 Children with Polycystic Kidney Disease

作　　者：张建涛[1] 汤淙鸿[1] 

机构地区：[1]广州市儿童医院,广东广州510120

出　　处：《国际医药卫生导报》2007年第16期84-86,共3页International Medicine and Health Guidance News

摘　　要：目的探讨小儿多囊肾的临床特点及诊断情况。方法回顾性分析1990年1月～2006年12月收治的33例多囊肾患儿的临床特点及诊疗情况。结果小儿多囊肾33例中男21例，女12例，年龄中位数为6．5岁。起病时的临床表现为尿异常22例、发热3例、腹部包块5例，余为面苍白、纳差、乏力、腹痛、多发畸形及抽搐。明确诊断时17，例存在肾功能异常。均经B超诊断为多囊肾。18例经长期随访，5例死亡，6例因终末期肾病而接受透析，3例肾功能正常。结论B超对小儿多囊肾的确诊具有特殊价值，对尿常规异常的患儿应常规B超检查是早发现多囊肾的关键。Objective To investigate clinical characteristics and early diagnosis of polycystic kidney disease（PKD） in children. Method Clinical data of patients admitted to our hospital from January 1990 to December 2006 was analyzed retrospectively for clinical characteristics, diagnosis and treatment. Result 21 boys and 12 girls were diagnosed as PKD at a median of 6. 5 years of age. Abdominal mass was found in 5 cases, abnormal urinalysis in 22 cases, febricity in 3 cases, and paleness, rhinorrhagia, poor appetite, fatigue, bellyache or seizure in the others. 17 of them had damaged renal function when being diagnosed. All patients were diagnosed by ultrasonography. Among 18 children who were followed up regularly, 5 died, 6 underwent dialysis due to end stage renal disease, 3 had normal renal function. Conclusion The majority of our patients were sutosomal recessive PKD. Clinical manifestations were various when they visited doctors. Ultrasonography should be applied to children with abnormal urinalysis for early diagnosis of PKD.

关 键 词：儿童 多囊肾临床分析 

分 类 号：R726[医药卫生—儿科]