孤立性心肌致密化不全超声心动图及临床特点探讨  

Initial study on the ultrasonic cardiogram and clinical characteristics of isolated ventricular noncompaction

作　　者：林苗[1] 杨丽翠[2] 王凯华[2] 黄旭梅[2] 施中平[2] 

机构地区：[1]温州医学院研究生部,325035 [2]浙江省温州市第二人民医院心内科

出　　处：《中国医师进修杂志（内科版）》2008年第3期16-19,共4页Chinese Journal of Postgraduates of Medicine

摘　　要：目的探讨孤立性心肌致密化不全（IVNC）患者的超声心动图（UCG）及临床特点。方法回顾性分析38例IVNC患者的UCG及临床表现，并对其中11例患者的23例直系亲属进行UCG检查。结果38例IVNC患者UCG检查均见受累心腔内不同程度异常隆突、粗大的肌小梁和其间深陷的隐窝影像，14例仅累及心尖部。23例直系亲属中发现1例左心扩大（LVE），1例扩张型心肌病（DCM）及2例无症状心尖IVNC。结论IVNC并非罕见，其发病年龄跨度大，临床病程迁延，临床表现各异，有家族发病倾向，似与DCM有遗传联系。同时IVNC具有特征性UCG改变，局限于心尖部位不少见，UCG是重要的诊断和筛查手段，尤其不应忽视对心尖部位的探查，以免误诊和漏诊。Objective To study the ultrasonic cardiogram （UCG） and chnical characteristics of isolated ventrieular non-compaction （IVNC）. Methods The UCG changes and clinical manifestations of 38 eases with IVNC were analyzed retrospectively, and 11 cases was examined in first-degree relatives of 23 patients by UCG. Results UCG showed numerous, excessively prominent trabeculae and deep trabeeula recesses in the ventrielular chambers of all the 38 eases, and in 14 of them the pathological changes only located on the apex of left ventricle. Through screening, 1 ease of left ventrieular enlargement was identified, 1 case of dilated eardiomyopathy and 2 eases of asymptomatic IVNC that focused on the left ventrieular apex. Conclusions IVNC is not rare. The age and the clinical manifestations of IVNC are quite different, and the nature history seems quite long. IVNC seems to have relationship with dilated eardiomyopathy. UCG is an important way for diagnosing or screening,as the UCG changes of IVNC are so characteristic. Doctors shouldn＇t ignore to check the apex area.

关 键 词：孤立性心肌致密化不全 超声心动描记术 临床特点 诊断 病例 

分 类 号：R542.2[医药卫生—心血管疾病] R540.45[医药卫生—内科学]