鲁登巴赫氏综合征和介入治疗技术——附2例报告  

Lutembacher's syndrome and percutaneous intervention therapy(a report of 2 cases)

作　　者：魏爱英[1] 刘建平[1] 李世珍 

机构地区：[1]山西省太原市解放军264医院,山西太原030001 [2]山西省太原市军区门诊部

出　　处：《罕少疾病杂志》2008年第2期29-32,共4页Journal of Rare and Uncommon Diseases

摘　　要：目的观察我国鲁登巴赫氏(Lutembacher)综合征的发病情况;关注医源性Lutembacher综合征的发生。方法检出1979年至2007年Lutembacher综合征在不同类型文献报道的分布以及随机33篇文献中6488例经皮穿刺气囊导管二尖瓣成形术(Percutaneous balloon mitral valvuloplasty,PBMV)的并发症患者的资料。结果1.我国28年间Lutembacher综合征发病总数352例;2.1995年至2007年Lutembacher综合征呈现增多及减少趋势,可能与经皮介入治疗技术(Percutaneous Intervention Therapy,PIT)的开展有关系。3.PBMV并发症之一,心房水平左向右分流71例,同样属于医源性Lutembacher综合征,未在Lutembacher综合征发病总数中。4.经典性和医源性Lutembacher综合征的治疗和发病有所不同。结论1.二尖瓣狭窄(Mitral Stenosis,MS)行PBMV后产生心房水平左向右分流应当诊断为医源性Lutembacher综合征并值得关注。2.关注我国医疗服务市场的准入制度进程;3.PBMV技术和部分Lutembacher综合征选用介入技术治疗具有前景,应进一步完善和规范。Objective To investigate the situation of Lutembacher＇ s syndrome in China and focus on the occurrence of the iatrogenic Lutembacher＇ s syndrome. Methods The literatures about the Lutembacher＇ s syndrome during 1979 and 2007 were collected and 33 papers on the Percutaneous Balloon Mitral Valvuloplasty（PBMV） complications were analyzed. Results 1. The total cases of the Lutembacher＇ s syndrome were 352 in 28 years.2.The Lutembacher＇ s syndrome appeared to be instable,which maybe had relation to the PBMV.3. One of the PBMV complications, 71 cases＇ level of atrium cordis with left-to-right shunt belonged to the iatrogenic Lutembacher＇ s syndrome,but it was not added up to the Lutembacher＇ s syndrome. 4.The treatment and the occurrence were different between the classical and iatrogenic Lutembacher＇ s syndrome. Conclusion 1. After PBMV is performed on the mitral stenosis, it must be diagnosed as iatrogenic Lutembacher＇ s syndrome if the level of artrium cordis with left-to-right shunt occurs. 2. The rules of medical service market must be paid attention to. 3. PBMV and Percutaneous Intervention Therapy have a good perspective in the treatment of some Lutembacher＇ s syndromes and need more perfection.

关 键 词：医源性Lutembacher综合征 经皮介入治疗技术 并发症 

分 类 号：R542.51[医药卫生—心血管疾病]