蝶枕部骨纤维异常增殖症1例并文献复习  

Fibrous dysplasia involving sphenoid and occipital bone:one case report and literature review

作　　者：刘珺[1,2] 孔维佳[1] 王彦君[1] 杨阳[1] 俞燕萍[1] 吴媛媛[1] 

机构地区：[1]华中科技大学同济医学院附属协和医院耳鼻咽喉科,武汉430022 [2]襄樊市中心医院耳鼻咽喉科,湖北襄樊441021

出　　处：《临床耳鼻咽喉头颈外科杂志》2008年第20期941-943,共3页Journal of Clinical Otorhinolaryngology Head And Neck Surgery

摘　　要：目的:探讨颅骨的骨纤维异常增殖症的临床表现、影像学特征、病理学改变、诊断和治疗。方法:报告1例蝶枕部骨纤维异常增殖症并复习文献。结果:颅骨的骨纤维异常增殖症以头痛、眼球突出、复视甚至失明等为主诉。其CT特征为"毛玻璃样变",骨纤维畸形、硬化及黏液囊性变。病理学检查可明确诊断,而其影像学的特征性改变也可为诊断提供有力的证据。结论:颅骨的骨纤维异常增殖症临床表现多样,容易误诊,需结合临床表现、影像学及病理学检查结果进行诊断。对骨纤维异常增殖症患者手术治疗应当慎重,以保留残存的功能为首要目的。Objective：To study the clinical manifestation, radiograph features, pathology, diagnosis and treatment of fibrous dysplasia in cranial bone. Method ： A case of fibrous dysplasia involving sphenoid and occipital is reported and literature were reviewed. Result： The most common complaint were headache, proptosis, diplopia, or visual changes. Distinguishing features of fibrous dysplasia on CT include ＂ground-glass＂ appearance, bone fiber anisotrophy, aneurysmal bone cyst formation and thickness of the cranial cortices. Fibrous dysplasia could be ex- actly diagnosed by pathology. Computed tomography was also a choice for diagnosis. Conclusion： Fibrous dysplasia involving the cranial bone can present in myriad ways. Modern imaging modalities and histopathologic analysis is required to make accurate diagnosis. Surgery, particularly in a challenging region such as sphenoid and occipital bone, should preserve the existing function for the patients with functional impairment or a cosmetic deformity.

关 键 词：蝶枕部 骨纤维异常增殖症 电子计算机断层摄影术 磁共振成像 

分 类 号：R445[医药卫生—影像医学与核医学]