50例右室双出口的外科治疗  

Surgical Correction of Double Outlet Right Ventricle in 50 Cases

作　　者：曹鼎方[1] 傅惟定[1] 苏肇伉[1] 丁文祥[1] 朱德明[1] 陈玲[1] 

机构地区：[1]上海第二医科大学附属新华医院小儿心胸外科,上海200092

出　　处：《心肺血管病杂志》1998年第2期112-114,共3页Journal of Cardiovascular and Pulmonary Diseases

摘　　要：我科自1986年7月至1996年4月外科治疗右室双出口（DORV）50例，早期死亡3例（6％）。本组病理解剖SDD型39例，SDL、SLL和ILL各为3、4和4例。主动脉下室缺30例，靠近和远离两大动脉开口的室映各7例，4例位于肺动脉下，2例不详。30例伴有肺动脉狭窄（PS）。DORV是一复杂先心病，为提高手术疗效，须仔细了解其病理解剖，作好手术设计方案。DORV无PS，易早期并发肺血管疾病，应在1岁前手术；并PS者，3-5岁手术为宜；如需用心外带瓣管道，应推迟至5-6岁。DORV外科治疗应据不同类型选择不同手术方法。This paper presents surgical correction of Double Outlet Right Ventricle (DORV) in 50 cases from July, 1986 to April, 1996. Three cases died early (6%). The pathologic anatomy of this group: SDD 39 cases,SDL, SLL and ILL 3, 4 and 4 cases respectively. Subaortic VSD 30 cases, doubly committed and noncommitted VSDs 7 cases each, subpulmonary VSD 4 cases, 2 cases unknown. Thirty cases were associated with pulmonary stenosis (PS). DORV is a complex congenital heart disease. To improve operative results, we must understand its pathologic anatomy thoroughly and make an operative designed protocol. DORV without PS develops pulmonary vascular disease early and should be operated upon before the age of 1 year. The optimal age for surgical correction of DORV with PS is 3 to 5 years. The surgical correction should be postponed until the age of 5 to 6 years if valved conduit is needed. Variable operative procedures are used for DORV correction according to its different type of pathologic anatomy.

关 键 词：心脏 右室双出口 病理解剖 治疗 外科手术 

分 类 号：R654.205[医药卫生—外科学]