Isolated non-compaction of ventricular myocardium in a victim of the Wenchuan earthquake with crush syndrome and acute renal failure  

作　　者：LIU Fang GAO Fa-bao FU Ping QIU Hong-yu HU Hong-de TANG Hong ZHANG Ling SONG Bin TANG Wan-xin TAO Ye HUANG Song-min 

机构地区：[1]Division of Nephrology , West China Hospital, Sichuan University, Chengdu, Sichuan 610041, China [2]Division of Radiology , West China Hospital, Sichuan University, Chengdu, Sichuan 610041, China [3]Division of Cardiology, West China Hospital, Sichuan University, Chengdu, Sichuan 610041, China

出　　处：《Chinese Medical Journal》2009年第18期2196-2198,共3页中华医学杂志（英文版）

摘　　要：Non-compaction of the ventricular myocardium （NVM） is a rare congenital genetic heart defect that was initially reported 17 years ago by means of autopsy; few cases have been published since then. It has been classified as the primary inherited cardiomyopathy by the American Heart Association Scientific Statement in 2006 under contemporary definitions and classification of cardiomyopathies. It is caused by an arrested development of muscle fiber compaction, a process that normally takes place dunng early embryogenesls, which is characterized by numerous sinusoids or trabeculae that are excessive in number and abnormal in prominence and by deep intratrabecular recesses covered by endothelium that exhibits continuity with ventricular endocardium. It usually involves one and/or more segments of the left ventricle, while the clinical manifestations are highly variable,Non-compaction of the ventricular myocardium （NVM） is a rare congenital genetic heart defect that was initially reported 17 years ago by means of autopsy; few cases have been published since then. It has been classified as the primary inherited cardiomyopathy by the American Heart Association Scientific Statement in 2006 under contemporary definitions and classification of cardiomyopathies. It is caused by an arrested development of muscle fiber compaction, a process that normally takes place dunng early embryogenesls, which is characterized by numerous sinusoids or trabeculae that are excessive in number and abnormal in prominence and by deep intratrabecular recesses covered by endothelium that exhibits continuity with ventricular endocardium. It usually involves one and/or more segments of the left ventricle, while the clinical manifestations are highly variable,

关 键 词：non-compaction cardiomyopathy crush syndrome acute renal failure EARTHQUAKE 

分 类 号：R686[医药卫生—骨科学]