紫绀型先天性心脏病临床病理分析(附15例尸检报告)  

Clinical and pathological analysis of cyanotic congenital heart disease:a report of 15 autopsy cases

作　　者：姚青[1] 魏晓莹[2] 李瑞平[2] 

机构地区：[1]江苏省中西医结合医院病理科,江苏南京210028 [2]东南大学附属中大医院病理科,江苏南京210009

出　　处：《东南大学学报（医学版）》2010年第5期505-508,共4页Journal of Southeast University(Medical Science Edition)

基　　金：国家自然科学基金资助项目(3047078);教育部博士点基金资助项目(20090092110053)

摘　　要：目的:分析紫绀型先天性心脏病的尸检病理解剖学特征,为临床诊断及治疗提供详尽的病理学指导。方法:收集15例紫绀型先天性心脏病尸检病例,应用心脏节段分析法进行解剖形态学观察描述。结果:15例紫绀型先天性心脏病中,完全性大动脉转位5例,法洛四联症5例,单心室3例,肺静脉畸形合并单心房1例,右心室发育不良综合征1例,其中3例合并有永存左上腔静脉。结论:紫绀型先天性心脏病具有复杂性,详尽的尸检资料有助于临床术前诊断及手术成功率的提高。Objective ： To explore the clinical and pathological characteristics of cyanotic congenital heart disease. Methods： 15 cases of cyanotic congenital heart disease were collected and studied by sequential segmental analysis. Results： There were 5 cases of complete transposition of the great arteries, 5 cases of tetralogy of Fallot, 3 cases of single ventricle, 1 case of hypoplastic right heart syndrome and 1 case of pulmonary stenosis with single auricle. 3 of the 15 cases were with persistent left superior vena cava. Conclusion： The cyanotic congenital heart disease has the characteristics of complexity. Detailed and completed autopsy information benefits the clinical diagnosis and surgical treatment of the disease.

关 键 词：先天性心脏病 病理 大动脉转位 法洛四联症 

分 类 号：R541.1[医药卫生—心血管疾病]