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出 处:《国际皮肤性病学杂志》2010年第6期319-321,共3页International Journal of Dermatology and Venereology
摘 要:皮肤异色病样淀粉样变是原发性皮肤淀粉样变的少见类型,国内外关于本病的报道较少;多种因素参与皮肤异色病样淀粉样变发病,明确诊断需组织病理的支持,必要时需行电镜观察,且需与有皮肤异色样变表现的其他疾病相鉴别.基于已报道的病例,就该病病因、临床特点、组织病理、诊断及鉴别诊断等方面进行探讨.Poikiloderma-like cutaneous amyloidosis is a rare variant of primary amyloidosis and has been seldom reported at home and abroad. Numerous factors are involved in the development of poikilodermalike cutaneous amyloidosis. Histopathology is essentially required for its diagnosis, and electron microscopy is sometimes needed. Differential diagnosis should include other diseases with poikilodermatous skin lesions. In view of reported cases, the authors describe the etiology, clinical features, histopathology, diagnosis and differential diagnosis of poikiloderma-like cutaneous amyloidosis.
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