Diffuse pulmonary lymphangiomatosis： a case report with literature review  

作　　者：DU Ming-hua YE Ruan-jian SUN Kun-kun LI Jian-feng SHEN Dan-hua WANG Jun GAO Zhan-cheng 

机构地区：[1]Department of Respiratory & Critical Care Medicine, Beijing University People's Hospital, Beijing 100044, China [2]Department of Pathology, Beijing University People's Hospital, Beijing 100044, China [3]Department of Thoracic Surgery , Beijing University People's Hospital, Beijing 100044, China1 [4]Department of Internal-Medicine, Fengning County Hospital, Fengning, Hebei, 068350 China

出　　处：《Chinese Medical Journal》2011年第5期797-800,共4页中华医学杂志（英文版）

摘　　要：Diffuse pulmonary lymphangiomatosis （DPL） is a rare disease that is characterized by diffuse proliferation of abnormal pulmonary lymphatic channels. DPL occurs mostly in children and young adults and often undergoes a progressive clinical course, eventually causing deterioration of the lung. Both the clinical diagnosis and treatment of DPL remain a challenge. Here, we report a case of DPL in a 53-year-old Chinese woman with comprehensive investigations including pulmonary function tests, computer tomography （CT）, bronchoscopy and histological examination of the lung biopsy, and review the literature.Diffuse pulmonary lymphangiomatosis （DPL） is a rare disease that is characterized by diffuse proliferation of abnormal pulmonary lymphatic channels. DPL occurs mostly in children and young adults and often undergoes a progressive clinical course, eventually causing deterioration of the lung. Both the clinical diagnosis and treatment of DPL remain a challenge. Here, we report a case of DPL in a 53-year-old Chinese woman with comprehensive investigations including pulmonary function tests, computer tomography （CT）, bronchoscopy and histological examination of the lung biopsy, and review the literature.

关 键 词：diffuse pulmonary lymphangiomatosis computer tomography b^vnchoscopy 

分 类 号：S858.292[农业科学—临床兽医学] G256[农业科学—兽医学]