婴儿左冠状动脉起源于肺动脉的诊断研究  

Left coronary artery arising from pulmonary artery in infants

作　　者：韩玲[1] 杜嘉会[1] 张桂珍[1] 罗毅[1] 裴金凤[1] 梁秋香[1] 金梅[1] 吴邦骏[1] 李磊[1] 刘虎[1] 梁永梅[1] 吴亚峰 

机构地区：[1]首都医科大学附属北京安贞医院,100029

出　　处：《中国实用儿科杂志》1999年第11期664-666,共3页Chinese Journal of Practical Pediatrics

摘　　要：目的　研究婴儿左冠状动脉起源于肺动脉（ＡＬＣＡＰＡ） 的临床特点及诊断方法。方法　总结分析１９９３～１９９８ 年收治的４ 例ＡＬＣＡＰＡ 的临床特点。结果　４ 例ＡＬＣＡＰＡ均初诊为婴儿心内膜弹力纤维增生症，发病年龄小于３ 个月，心电图Ｉ，ａＶＬ，Ｖ４～６ 导联出现异常Ｑ 波，彩色多普勒超声心动图检查示左冠状动脉缺如。最后经导管检查及心血管造影确诊。结论　本文提出的诊断方法有助于婴儿ＡＬＣＡＰＡ的诊断，且易为儿科医师掌握。Objective\ To recognize the disease of anomallous origin of left coronary artery from pulmonary artery(ALCAPA).Methods\ The clinical manifestations of four cases of ALCAPA who were hospitalized from 1993 to 1998 in Anzhen Hospital were analyzed.Results\ ①The symptoms of four cases of ALCAPA are like myocarditis,cardiomyopathy or endocardiofibroelastosis.②The onset age is less than 3m.③Characteristic ECG findings are the abnormal Q wave in lead I.avL and V 4～6 .④UCG may show the abnormal origin of left coronary artery.⑤The final diagnosis can be achieved by the catheterization and selective angiocardiography.Conclusion\ The diagnosis is not difficult and there is improvement in the survival of infants who have surgical correction.

关 键 词：先天性 冠状动脉畸形 肺动脉 婴儿 

分 类 号：R725.433[医药卫生—儿科]