Cantrell综合征的诊断与治疗  

Clinic diagnosis and treatment of patients with Cantrell syndrome

作　　者：孙明利[1] 吕滨[1] 荆志成 杨新令[1] 于方方[1] 李世国[1] 蒋世良[1] 戴汝平[1] 

机构地区：[1]北京协和医学院中国医学科学院北京阜外心血管病医院放射科,100037 [2]上海肺科医院心内科

出　　处：《中华心血管病杂志》2011年第9期836-839,共4页Chinese Journal of Cardiology

摘　　要：目的探讨Cantrell综合征的诊断、治疗与预后。方法回顾性分析5例临床诊断为Cantrell综合征患者的临床、影像学、手术及随访材料，总结Cantrell综合征的临床特征。结果5例患者年龄7d-76岁。3例有Cantrell综合征的5种畸形，术前准确诊断并经手术证实。1例术后60个月死亡，2例存活（分别随访43个月和4个月）。2例仅有Cantrell综合征的部分畸形（左心室憩室形成）。1例非完全性Cantrell综合征经手术证实，另1例为影像学发现，分别随访75个月和64个月均健在。结论随着现代影像学技术的发展，Cantrell综合征术前诊断不难，及时治疗可改善预后。Objective To analyze the diagnostic feature, treatment and prognosis of patients with Cantrell syndrome. Methods Clinical manifestation, diagnosis, operation and follow-up data of 5 patients with Cantrell syndrome were summarized in this retrospective analysis. Results The age of the 5 patients was 7 days-76 years, definite diagnosis was made in 3 cases and 2 cases presented feature of incomplete Cantrell syndrome. Three patients with full Cantrell syndrome were correctly diagnosed before operation and confirmed by operation. One patient with incomplete Cantrell syndrome （two-vessel stenosis ） received bypass surgery. Another asymptomatic patient with incomplete Cantrell syndrome （ apical diverticulum of the left ventricle） does not need operation and is under observation. Daring follow-up, 1 patient died at 60 months after operation and the remaining 4 patients are alive and well. Conclusions With the development of modern imaging technology, it becomes easy to make correct diagnose Cantrell syndrome before operation. Prognosis is fine post timely operation and related intervention.

关 键 词：CANTRELL综合征 诊断 预后 

分 类 号：R541.1[医药卫生—心血管疾病]