肺泡蛋白沉积症的研究现状  

Research Status of Pulmonary Alveolar Proteinosis

作　　者：彭刚[1] 孙希文[1] 

机构地区：[1]同济大学医学院附属上海市肺科医院影像科,上海200433

出　　处：《医学综述》2012年第8期1146-1148,共3页Medical Recapitulate

摘　　要：肺泡蛋白沉积症(PAP)是一种以肺泡腔及终末呼吸性细支气管内堆积过量的磷脂蛋白样物质为特征的弥漫性肺部疾病,其起病隐匿,发病机制不明,临床表现缺乏特异性。CT表现以"地图样"分布的磨玻璃影和"碎路石征"为特征。支气管肺泡灌洗是治疗本病的最佳方法。发病机制方面的深入研究为本病的诊断和治疗开辟了新的前景。Pulmonary alveolar proteinosis is a diffuse lung disease,characteristized by the excessive phospholipids protein kind material accumulated in alveolar space and terminal respiratory bronchiols,with concealed onset and unclear pathogenesis,and unspecific clinical manifestations.The features of CT manifestations were ground-glass opacity and crazy paving appearance.Bronchoalveolar lavage was the best method of treatment.The deeper research of pathogenesis opened up a new prospect for the diagnosis and treatment.

关 键 词：肺泡蛋白沉积症 发病机制 体层摄影术 X线计算机 

分 类 号：R816.41[医药卫生—放射医学]