原发淀粉样变病的胸部表现(附九例报告)  

Radiographic findings of thorax in primary amyloidosis (analysis of 9 cases)

作　　者：宋伟 严洪珍 王云 

机构地区：[1]中国医学科学院协和医科大学协和医院放射科,北京100730

出　　处：《中华放射学杂志》2000年第3期196-198,共3页Chinese Journal of Radiology

摘　　要：目的　分析原发淀粉样变病累及胸部的影像学表现。方法　 5例局限性病变患者均行X线胸片、气管分叉体层及支气管镜检查 ,其中 3例做了CT检查 ;4例全身性病变患者行X线胸片、CT及超声心动图检查。 2例经尸检 ,7例经全身多部位组织活检证实。结果　 5例局限性病变患者均有气管支气管树的狭窄或闭塞 ,其中 2例分别合并左舌叶与右上叶阻塞性肺不张 ;4例全身性病变患者中肺间质病变 3例 ,胸膜增厚 4例 ,胸腔积液 4例 ,室间隔与左心室肌增厚 3例 ,心包积液 1例。结论　局限于气管支气管树的原发淀粉样变病具有一定的影像特点 ,而全身性原发淀粉样变病累及胸部的有关影像学表现缺乏特征性 。Objective To analyze the radiographic findings of thorax in the patients with primary amyloidosis. Methods The radiography, CT, and echocardiography findings of 4 patients with primary systemic amyloidosis, and the radiography, tomography, bronchoscopy, and CT findings of 5 patients with primary localized amyloidosis were analyzed. Results Stenosis or occlusion of bronchotracheal tree were observed in 5 patients with localized amyloidosis; Among 4 patients with systemic amyloidosis, 3 cases of pulmonary interstitial involvement, 4 cases of pleural thickening, 4 cases of pleural effusion, 3 cases of interventricular septum and ventricular walls thickening , 1 case of pericardial effusion were observed. Conclusion The primary localized amyloidosis of bronchotracheal tree have characteristic radiographic findings, but the primary systemic amyloidosis have no distinctive radiographic findings, the diagnosis relies on pathology.

关 键 词：淀粉样变 CT 胸部表现 

分 类 号：R445[医药卫生—影像医学与核医学]