以突发性聋为首发表现的斜坡脊索瘤1例  

A case of clivus chordoma with first appearance of sudden deafness

作　　者：管华[1] 马志红[1] 郁葱颖[2] 

机构地区：[1]承德市中心医院耳鼻咽喉科,河北承德067000 [2]承德市中心医院病理科

出　　处：《临床耳鼻咽喉头颈外科杂志》2012年第13期617-617,623,共2页Journal of Clinical Otorhinolaryngology Head And Neck Surgery

摘　　要：1病例报告患者,女,55岁,右耳突发听力下降伴耳鸣1d于2010年2月23日入院。患者无眩晕、耳痛及耳溢液。既往有糖尿病史20余年,高血压病史10余年。体检：BP 150/90 mm Hg（1 mm Hg=0.133kPa）,双耳廓无畸形,外耳道通畅,鼓膜完整,内陷。纯音测听示：右耳全聋。Summary The patient was hospitalized for sudden hearing impairment for one day.Physical examination： the blood pressure was 150/90mmHg,the tympanic membranes in both ears were complete and otopiesis.Audiogram showed total deafness in the right ear and slight sensorineural deafness at speech frequency and 80db for high tone air conduction and 70db for bone conduction at high frequency in left ear.Tympanogram showed＂A＂ type in both ears and the ipsilateral and contralateral acoustic reflex in both ears were not induced.BAEP showed that the V wave threshold on the right was not induced and it was 50dbnHL on the left.CT showed a limited low density area in the clivus.MRI showed a space-occupying lesion behind the basilar clivus and ahead of brain stem.Pathological examination showed CK（＋）,EMA（＋）,S-100（＋）according to immunohistochemistry,which was in accordance with chondroid chordoma.Diagnosis：chondroid chordoma of clivus.

关 键 词：聋 突发性 斜坡脊索瘤 

分 类 号：R764.437[医药卫生—耳鼻咽喉科]