成人噬血细胞性淋巴组织细胞增多症一例并文献复习  

A case report of adult hemophagocytic lymphohistiocytosis and literature review

作　　者：关欣[1] 韩淑玲[1] 王宽婷[1] 杨婧[1] 方志坚[1] 高乃姝[1] 

机构地区：[1]北京大学首钢医院风湿免疫科,北京100144

出　　处：《临床和实验医学杂志》2012年第13期1005-1007,共3页Journal of Clinical and Experimental Medicine

摘　　要：目的探讨噬血细胞性淋巴组织细胞增多症(HLH)的临床特点、发病机制、治疗方案及预后。方法回顾分析1例成人HLH患者的临床资料并进行文献复习。结果患者经积极规范治疗,病情明显好转。结论 HLH病情凶险,进展迅速,早期积极治疗可以治愈。Objective To explore the clinical characteristics,pathogenesis,treatment and prognosis of hemophagocytic lymphohistiocytosis（HLH）.Methods The clinical data of an adult patient with HLH were retrospectively reviewed and anlyzed in combination with review of related literatures.Results The situation of this patient with HLH was significantly improved after active treatment.Conclusion HLH is a rapidly progressive and fatal disease,but it can be cured with early diagnosis and effective treatment.

关 键 词：淋巴组织细胞增多症 噬血细胞性 治疗 预后 

分 类 号：R55[医药卫生—血液循环系统疾病]