坏死性结节病样肉芽肿病  

Necrotizing sarcoid granulomatosis

作　　者：黄海东[1] 白冲[1] 李强[1] 

机构地区：[1]第二军医大学附属长海医院呼吸内科,上海200433

出　　处：《中国实用内科杂志》2012年第11期853-855,I0001,共4页Chinese Journal of Practical Internal Medicine

摘　　要：坏死性结节病样肉芽肿病是一种临床罕见的肺部肉芽肿性疾病。临床表现无特异性。该病典型病理学特征包括肺内非干酪样上皮细胞性肉芽肿、肉芽肿性血管炎和凝固性坏死。鉴别诊断主要包括结节病、Wegener肉芽肿以及感染性疾病所致的肉芽肿性疾病。该病对糖皮质激素治疗敏感,病情反复者需加强随访。Necrotizing sarcoid granulomatosis （NSG） is a seldom seen pulmonary guanulomatous disease ,with no specificity of clinical manifestation. The typical pathological characteristics of NSG include non-caseous epithelial granulomatosis, granulomatous angiitis and coagulation necrosis. The differential diagnosis of NSG mainly include sarcoidosis ,wegener granulomatosis and other guanulornatous diseases caused by infectious diseases. This disease is sensitive to the glucoeorticoid treatment. The following-up should be enhanced among those patients with relapse of NSG.

关 键 词：坏死性结节病样肉芽肿病 结节病 肉芽肿 

分 类 号：R543[医药卫生—心血管疾病]