胎儿超声心动图诊断埃布斯坦综合征  

Fetal echocardiography in diagnosis of Ebstein anomaly

作　　者：谷孝艳[1] 何怡华[1] 张烨[1] 韩建成[1] 陈娇阳[1] 李治安[1] 

机构地区：[1]首都医科大学附属北京安贞医院超声科,北京100029

出　　处：《中国医学影像技术》2013年第9期1526-1529,共4页Chinese Journal of Medical Imaging Technology

基　　金：国家自然科学基金(81171350);北京市教育委员会重点项目(KZ201210025029);北京市自然科学基金(7122059)

摘　　要：目的探讨胎儿超声心动图诊断埃布斯坦综合征及其并发症的价值。方法 2450胎接受胎儿超声心动图检查;对其中的14胎埃布斯坦综合征胎儿的超声心动图进行分析,并与大体病理结果进行对照分析。结果 14胎埃布斯坦综合征胎儿中,超声均显示三尖瓣反流,其中重度11胎(11/14,78.57%);7胎(7/14,50.00%)合并肺动脉瓣狭窄;3胎(3/14,21.43%)肺动脉内径与主动脉内径比>1.1;1胎合并心脏其他畸形;7胎伴胸腔、腹腔及心包积液共。结论埃布斯坦综合征胎儿易并发重度三尖瓣反流、肺动脉瓣狭窄、肺动脉与主动脉比例变小、胸腔/腹腔/心包积液;胎儿超声心动图对埃布斯坦综合征胎儿的细化诊断是判断预后的重要依据。Objective To observe the value of fetal echocardiography in diagnosis of Ebstein abnormalitiy and combined complications. Methods Fourteen fetus with Ebstein anomaly from 2450 fetal echocardiography examinations were ana- lyzed. Results Echocardiography showed all the fetuses with Ebstein anomaly had tricuspid regurgitation, 11 （11/14, 78.57 %） had severe tricuspid regurgitation, 7 （7/14,50.00 %） had pulmonary stenosis, the ratio of pulmonary and aorta diameter was larger than 1.1 in 3 fetuses （3/14,21.43 %）. One fetus combined with other cardiac deformation, 7 had pleu- ral effusion, ascites or perieardial effusion. Conclusion Severe tricuspid regurgitation, pulmonary stenosis/hypoplasia,the decreased ratio of pulmonary and aorta diameter and pleural effusion/ascites/pericardial effusion are common in fetuses with Ebstein anomaly. Fetal echocardiography plays a key role in the detailed diagnosis and prognosis evaluation.

关 键 词：胎儿 超声心动描记术 埃布斯坦综合征 预后 

分 类 号：R540.4[医药卫生—心血管疾病] R541.1[医药卫生—内科学]