先天性肺囊性疾病的研究现状  

Congenital cystic lung lesions:A review

作　　者：欧姜凤 彭东红[1] 

机构地区：[1]重庆医科大学附属儿童医院呼吸中心,重庆400014

出　　处：《中国现代医生》2014年第8期158-160,共3页China Modern Doctor

摘　　要：先天性肺囊性疾病是一种较少见的先天性肺发育异常,包括先天性囊性腺瘤样畸形、支气管源性肺囊肿、先天性大叶性肺气肿、肺隔离症四型。发病机制尚不明确,但各具特点。临床表现相似。胸部X线及CT为国内主要诊断手段,国外则多为产前超声。尽早手术切除为治疗首选,手术时机、手术方式及手术范围的选择一直存在争议。本文仅对此类疾病的研究现状作一综述。Congenital cystic lung lesions are a group of congenital pulmonary dysplasia with low incidence, which in- clude congenital cystic adenomatoid malformation （CCAM）, bronchogenic cyst,congenital lobar emphysema （CLE）, and pulmonary sequestration （PS）.The pathogenses are still obscure and different.But they have similar manifestations.In china, chest X-ray and computed tomography after birth are the key methods for diagnosis, while prenatal ultrasound in a foreign country. Surgical resection as early as possible is preferred, but the choices of the operation time methods and scope have been controversial. The current situation of these diseases is reviewed in this article.

关 键 词：先天性囊性腺瘤样畸形 支气管源性肺囊肿 先天性大叶性肺气肿 肺隔离症 

分 类 号：R682.16[医药卫生—骨科学]