MSCT诊断Abernethy畸形  

MSCT in diagnosis of Abernethy malformation

作　　者：高军[1] 于彤[1] 刘志敏[1] 刘勇[1] 段晓岷[1] 彭芸[1] 曾津津[1] 

机构地区：[1]首都医科大学附属北京儿童医院影像中心,北京100045

出　　处：《中国医学影像技术》2014年第5期649-652,共4页Chinese Journal of Medical Imaging Technology

基　　金：首都医学发展基金(2009-2077);科技重大专项项目(2011ZX09302-007-01)

摘　　要：目的分析Abernethy畸形的临床及MSCT资料,以提高对该类畸形的认识。方法收集11例Abernethy畸形患儿,分别接受CT平扫及增强扫描,分析其影像学表现。结果 Abernethy I型患儿5例,影像学特点为肝门静脉无明确显示,3例胃肠道回流血液通过肠系膜下静脉、1例经左侧肾静脉引流至下腔静脉;1例通过腰升静脉进入半奇静脉,回流至上腔静脉。Abernethy畸形Ⅱ型患儿6例,影像学特点为肝内门静脉分支细、少,胃肠回流血液部分通过门静脉入肝,5例通过肠系膜下静脉、1例通过肠系膜上静脉汇入下腔静脉。结论 Abernethy畸形是较罕见的先天性疾病,MSCT是诊断本病的主要影像学手段。Objective To analyze clinical and MSCT data of Abernethy malformation patients, so as to improve the un-derstanding of Abernethy malformation. Methods Totally 11 patients with Abernethy malformation who underwent con-ventional CT and contrast-enhanced scanning were enrolled. Results Imaging features of 5 patients with Abernethy malfor-mation Ⅰ included invisible hepatic portal vein and gastrointestinal blood draining into inferior vena cava through the dilated inferior mesenteric vein （n=3）, left renal vein （n=1）, and draining into superior vena cava through ascending lumber vein and hemiazygos vein （n=1）, while of 6 patients with Abernethy malformation Ⅱ included narrowed intrahepatic portal vein and extrahepatic portal vein, some gastrointestinal blood draining into the liver through portal vein and at the same time through the dilated inferior mesenteric vein （n=5）, superior mesenterie vein （n=1） draining into the vena cava. Con-elusion Abernethy malformation is a relatively rare congenital disease, and MSCT may be regarded as the main imaging method for diagnose of this disease.

关 键 词：ABERNETHY畸形 门体静脉分流 体层摄影术 X线计算机 

分 类 号：R726.2[医药卫生—儿科] R814.42[医药卫生—临床医学]