成人特发性肺含铁血黄素沉着症的诊治分析:附病例报道  

Diagnosis and Therapy of Adult Idiopathic Pulmonary Hemosiderosis:A Case Report

作　　者：孙贝贝[1] 吴纪珍[1] 马利军[1] 

机构地区：[1]郑州大学人民医院呼吸科,河南省郑州市450000

出　　处：《中国全科医学》2014年第14期1654-1658,共5页Chinese General Practice

摘　　要：特发性肺含铁血黄素沉着症是一种原因不明的肺泡毛细血管出血性疾病,多发于儿童,成人发病率极低,但误诊率高、预后差、病死率高。病变进程因人而异,发病机制尚不确切,治疗措施有限且存在争议。本文报道了1例成年女性特发性含铁血黄素沉着症患者的诊治资料,同时总结复习了国内外的相关文献,以期帮助临床医师提高对成人特发性肺含铁血黄素沉着症的理解与认识。Idiopathic pulmonary hemosiderosis（IPH）,a noncausal diffuse alveolar hemorrhage,often appears in children,rarely in adults,but with high misdiagnosis rate,poor prognosis and high fatality rate in adult.The disease process varies with each individual,and its pathogenesis is still unknown.Treatments for it are limited and remain disputed.This paper analyzes the clinical data of an adult woman with IPH and reviews relevant literatures both at home and abroad,to improve clinicians＇ understanding and awareness about IPH.

关 键 词：成人 特发性含铁血黄素沉着症 病例报告 

分 类 号：R543.7[医药卫生—心血管疾病]