与骨髓增生异常综合征相关的Sweet综合征的临床分析  被引量:3

Sweet's Syndrome with Pulmonary Involvement in Association with Myelodysplastic Syndrome

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作  者:陈芳源[1] 黄洪晖[1] 韩洁英[1] 宣正华[1] 陈小龙[1] 欧阳仁荣[1] 

机构地区:[1]上海第二医科大学仁济医院血液科,上海200001

出  处:《上海第二医科大学学报》2001年第2期158-160,共3页Acta Universitatis Medicinalis Secondae Shanghai

摘  要:目的提高与骨髓增生异常综合征 (MDS)相关的Sweet综合征的 (SS)认识。 方法报道 1例SS伴肺部浸润的MDS ,并做文献复习。 结果SS可出现在MDS之前 ,也可与MDS同时出现。中性粒细胞常增高 ,可有贫血、血小板减少。除皮肤浸润外 ,可侵犯全身其他脏器。 结论MDS合并SS伴肺部浸润易出现呼吸困难 ,预后不佳。Objective To introduce Sweet's syndrome (SS) associated with myelodysplastic syndrome (MDS). A case of SS with pulmonary involvement associated with MDS is stu died and reviewed with relevant literatures. SS may precede or occur with MDS. The patients suffer frequent by from neutrophilia, anemia and thrombocytopenia. In addition to the skin, other organs may also be involved. SS with pulmonary involvement associated with MDS is prone to suffer from dyspenia. The prognosis is very poor.

关 键 词:SWEET综合征 肺部浸润 骨髓增生异常综合征 临床分析 

分 类 号:R551.3[医药卫生—血液循环系统疾病] R733.7[医药卫生—内科学]

 

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