先天性无子宫无阴道9例的核磁共振检查分析  

Analysis of magnetic resonance for 9 cases of Mayer-Rokitansky-Kuster-Hauser syndrome

作　　者：王琨[1,2] 罗琼[1] 杨伟洪[3] 肖立[2] 刘蓓[1,2] 

机构地区：[1]香港大学深圳医院妇产科,深圳518000 [2]深圳市妇幼保健院妇产科 [3]香港大学深圳医院放射科

出　　处：《山西医科大学学报》2014年第6期489-492,共4页Journal of Shanxi Medical University

摘　　要：目的探讨先天性无子宫无阴道的原发性闭经患者的核磁共振检查结果。方法 9名年轻女性行磁共振检查,由妇科医生及放射线医生共同评价苗勒氏管、阴道、卵巢和其他发现。结果全部病例盆腔内都发现双侧始基子宫,其中1例有单侧的宫腔。始基子宫平均长径(2.73±0.68)cm。在全部病例中,两侧始基子宫之间由纤维带状结构连接。在7个病例中,带状结构交汇于位于膀胱上方靠近中央的三角软组织。8例有阴道下1/3存在。9例在始基子宫附近有双侧正常卵巢组织。1例单侧盆腔肾,2例第五腰椎骶骨化。结论在先天性无子宫无阴道综合征的病人中典型的苗勒氏管残存结构表现为由纤维带状组织连接的双侧始基子宫,两侧组织在膀胱上方的三角形软组织中线处汇合。Objective To explore the findings of magnetic resonance imaging（MRI） in patients with Mayer-Rokitansky-Kuster-Hanser （MRKH） syndrome. Methods Nine young females underwent MRI. One gynecologic and one radiologist reached consensus decisions for the evaluation of Mullerian remnants,vagina,ovaries,and associated findings. Results All cases had bilateral uterine buds in the pelvic cavity, and one had unilateral uterine cavity. The buds had an average long-axis diameter of （2.73 ＋ O. 68）cm. In all cases, bilat- eral buds were connected with fibrous band-like structures. In 7 cases, the band-like structures converged at the midline or a paramedian triangular soft tissue lying above the bladder dome. The lower one-third of the vagina was identified in 8 cases. All cases showed bilater- al normal ovaries near the uterine buds. one of unilateral pelvic kidney and two cases of lumbar sacralization were found. Conclusion Typical Mullerian remnants in MRKH syndrome consist of bilateral uterine buds connected by the fibrous band like structures ,which converge at the midline triangular soft tissue lying above the bladder dome.

关 键 词：闭经 磁共振成像 先天性无子宫无阴道综合征 苗勒氏管 

分 类 号：R711.1[医药卫生—妇产科学]