特发性腹膜后纤维化误诊为肾癌1例报告并文献复习  

Idiopathic retroperitoneal fibrosis misdiagnosed as renal cancer: a case report and literature review

作　　者：王维宁[1] 王艳波[1] 马小波[2] 于海东[3] 王春喜[1] 

机构地区：[1]吉林大学白求恩第一医院泌尿外科,吉林长春130021 [2]吉林大学白求恩第一医院病理科,吉林长春130021 [3]敦化市医院泌尿外科,吉林敦化133700

出　　处：《南方医科大学学报》2014年第11期1658-1660,共3页Journal of Southern Medical University

基　　金：国家自然科学基金(51403074);吉林省卫生厅青年基金(2013Q026)~~

摘　　要：目的通过具体病例并结合文献复习提高对特发性腹膜后纤维化疾病的认识。方法通过回顾我科1例特发性腹膜后纤维化的诊治并查阅相关文献,就特发性腹膜后纤维化的诊治进行复习总结。结果患者,男,51岁,因检查发现右肾占位性病变3 d入院。CT示右肾肾盂、肾盂输尿管移行处团块状软组织密度影,临床诊断为右肾癌,行后腹腔镜右肾根治性切除术,病理回报为特发性腹膜后纤维化。特发性腹膜后纤维化发病机制尚不确切,临床表现不典型,影像学检查具有一定特异性,治疗上根据具体情况可选择药物或手术治疗。结论腹膜后纤维化发病率低、误诊率较高。影像学辅助检查是主要诊断手段,具有一定特异性。A 51-year-old male patient was presented to our hospital for inspection of right renal space-occupying lesions. CT revealed soft tissue density in the right renal pelvis and renal pelvis ureter transitional crumb, for which a clinical diagnosis of right renal cancer was made. After laparoscopic radical resection of the right kidney; pathological examination supported the diagnosis of idiopathic retroperitoneal fibrosis. With an unclear pathogenesis, idiopathic retroperitoneal fibrosis presents with atypical clinical manifestations but shows specific features in imaging examination. Its treatment is individualized according to the specific condition for which conservative medical or surgical treatment can be considered. Retroperitoneal fibrosis has a low incidence and a high misdiagnosis rate, and imaging examinations remain currently the primary modality for diagnosis with specific findings.

关 键 词：特发性腹膜后纤维化 误诊 影像学辅助检查 

分 类 号：R699.2[医药卫生—泌尿科学]