成人特发性肺含铁血黄素沉着症1例报道及文献分析  

A case report of adult idiopathic pulmonary hemosiderosis and literature review

作　　者：卢立国[1] 闫卫彬[1] 孙婷婷[1] 韩光[1] 胡玉兰[1] 严明月 

机构地区：[1]江苏省沭阳县人民医院,223600

出　　处：《齐齐哈尔医学院学报》2015年第2期236-238,共3页Journal of Qiqihar Medical University

摘　　要：目的探讨成人特发性肺含铁血黄素沉着症(idiopathic pulmonary hemosiderosis,IPH)的病因、临床症状、影像学特点及治疗方法。方法本例患者采用支气管镜肺活检确诊,病例资料完整,同时结合国内外文献进行综合性回顾分析。结果本例患者为45岁成年女性,经支气管镜肺活检确诊为弥漫性肺泡出血(diffuse alveolar hemorrhage,DPH),同时实验室检查排除其他DPH,确诊为IPH,予糖皮质激素治疗效果好,经随访观察未复发。结论特发性肺含铁血黄素沉着症是一种少见、病因未明的弥漫性肺泡出血综合征,多见于儿童,急性期激素治疗效果好,成人预后较儿童好。Objective Discuss the pathogenesis,clinical symptoms,imaging and therapy of idiopathic pulmonary hemosiderosis（ IPH）. Methods The case of this report was diagnosed by bronchoscope,the data was complete,and review the domestic and overseas literature. Results The case was a 45-year-old woman,was confirmed diffuse alveolar hemorrhage（ DPH） by bronchoscope,other DPH was excluded by laboratory examination,the glucocorticoid therapeutic effect was satisfactory,and there was no relapse during the follow-up observation. Conclusions IPH is a disease of DPH which is rare and agnogenic,it occurs in child more often,the hormonotherapy is satisfactory,the prognosis in adult is better than in child.

关 键 词：特发性肺含铁血黄素沉着症 弥漫性肺泡出血 激素治疗 

分 类 号：R563.7[医药卫生—呼吸系统]