肱骨及尺桡骨罕见发育畸形的影像特征分析  

Imaging features of humerus, radius and ulna rare malformation

作　　者：陈勇[1] 刘杰[1] 丁建平[1] 李玉清[2] 

机构地区：[1]杭州师范大学附属医院放射科,310015 [2]河北省河北医科大学第三医院

出　　处：《中华医学杂志》2015年第13期1021-1023,共3页National Medical Journal of China

摘　　要：目的分析肱骨及尺桡骨罕见发育畸形的影像特征。方法回顾性分析1958-2014年问杭州师范大学附属医院和河北医科大学第三医院收治的40例肱骨及尺桡骨罕见发育畸形患者的影像及临床资料。以Swanson分类法为依据，将不同类型发育畸形的影像改变进行分类和总结。结果40例肱骨及尺桡骨罕见发育畸形中男19例、女21例，年龄18d～51岁，平均年龄（11．6±11．5）岁；共10种畸形，以Swanson分类，尺桡骨：形成障碍9例，为桡骨缺损；分化障碍分别为先天性上尺桡骨融合6例，Madelung畸形12例，先天性桡骨小头脱位4例；重复畸形2例，为双尺骨畸形；过度生长2例，为长尺短桡畸形；发育不全1例，为短肢畸形。肱骨和尺桡骨多骨受累：分化障碍1例，为肱桡骨融合；形成障碍1例，为无肢畸形。仍有1种畸形无法准确分类，为肘髌骨2例。结论肱骨及尺桡骨发育畸形种类较多且发病率不高，只有全面认识不同畸形的分类和特点，并结合典型的影像学表现，才能得出正确诊断避免误诊。Objective To investigate the imaging features of humerus, radius and ulna rare malformation. Methods A retrospective analysis of the clinical data and image of 40 cases of humerus and the radius and ulna rare developmental deformity andadmitted to hospital affiliated to 1958 -2014 years in The Affiliated Hospital of Hangzhou Normal University and the Third Hospital of Hebei Medical University. Take the Swanson classification as the basis, the image changes of different types of malformations are classified and summarized. Results 40 cases of humerus , radius and ulna rare malformation in 19 males and 21 females, age 18 days to 51 years, mean age （11.6 ± 11.5） years; a total of 10 kinds of deformities to Swanson classification, radius and ulna： failure of formation of parts 9 cases, for radial defect; failure of differentiation are congenital radioulnar synostosis 6 cases, Madelung＇s deformity 12 cases, congenital radial head dislocation 4 cases; duplication 2 cases, for double ulna syndrome; overgrowth 2 cases, as long ulna short radial deformity; undergrowth 1 case, for the micromelia. Humerus and ulna bony involvement： failure of differentiation 1 case, for brachial radial synostosis; failure of formation of parts 1 case, for amelia. There is still one kind of deformity can not be accurately classified as patella cubiti 2 cases. Conclusions Humerus, radius and ulna although more types of malformations and the incidence rate is not high, only a comprehensive understanding of different deformity classification and characteristics, combined with the typical imaging findings in order to arrive at a correct diagnosis to avoid misdiagnosis.

关 键 词：肱骨 桡骨 尺骨 发育畸形 

分 类 号：R682.1[医药卫生—骨科学]