系统性红斑狼疮合并血栓性微血管病  

The diagnosis and management of systemic lupus erythematosus associated thrombotic microangiopathy

作　　者：陈志威[1] 叶霜[1] 

机构地区：[1]上海交通大学医学院附属仁济医院南院风湿科,上海200001

出　　处：《中国实用内科杂志》2015年第10期825-827,共3页Chinese Journal of Practical Internal Medicine

摘　　要：血栓性微血管病是一种预后极差的严重的临床病理综合征,可与结缔组织病相关,如系统性红斑狼疮、系统性硬化及抗磷脂抗体综合征等。系统性红斑狼疮合并血栓性微血管病病死率高,对系统性红斑狼疮合并血栓性微血管病的早期诊断和治疗,尤显重要。Thrombotic microangiopathy（TMA） is a rare, life-threatening clinical pathological syndrome. The cause of TMA could be associated with multiple connective tissue diseases, including systemic lupus erythematosus（SLE）, systemic sclerosis（SSc）, and antiphospholipid syndrome（APS）. SLE-associated TMA is a severe disorder with high mortally. And early diagnosis and treatment of SLE-associated TMA is important and may improve the outcomes.

关 键 词：血栓性微血管病 系统性红斑狼疮 血浆置换 抗磷脂抗体综合征 

分 类 号：R593.2[医药卫生—内科学]