罕见的肥厚型心肌病合并巨大肺动脉瘤1例  

One case for hypertrophic cardiomyopathy complicated with huge pulmonary artery aneurysm

作　　者：李辉[1] 孙福成[1] 

机构地区：[1]北京医院心内科,北京100730

出　　处：《临床心血管病杂志》2016年第1期101-102,共2页Journal of Clinical Cardiology

摘　　要：肥厚型心肌病是常染色体显性遗传的心肌病,表现为心室的肥厚、心室充盈受限和顺应性的下降。而肺动脉瘤是一种罕见的心血管疾病,表现为肺动脉的异常扩张,可导致严重的心血管事件,包括心力衰竭、咯血、动脉瘤破裂、猝死等。我们确诊1例罕见的肥厚型心肌病合并肺动脉瘤患者,其病程长达20余年,具体病史见下。1病例资料患者,男,84岁,因＂活动后胸闷气短20余年,加重2个月＂就诊。Hypertrophic cardiomyopathy is an autosomal dominant inheritance cardiomyopathy.Pulmonary artery aneurysm is a rare cardiovascular disease with pulmonary artery aneurysmal dilation and subsequent severe cardiovascular events.We found a patient with these two diseases for over 20 years.The patient＇s huge pulmonary artery aneurysm may be due to hypertrophic cardiomyopathy and her autoimmune disease-psoriasis.

关 键 词：肥厚型心肌病 肺动脉瘤 自身免疫疾病 银屑病 

分 类 号：R542.2[医药卫生—心血管疾病]