先天性肺动静脉瘘  

Congenital pulmonary arteriovenous fistula

作　　者：刘瀚旻[1] 陈莉娜[1] 

机构地区：[1]四川大学华西第二医院儿童呼吸科,出生缺陷与相关妇儿疾病教育部重点实验室,成都610041

出　　处：《中华实用儿科临床杂志》2016年第16期1216-1218,共3页Chinese Journal of Applied Clinical Pediatrics

摘　　要：先天性肺动静脉瘘是一种临床罕见的肺血管异常，以肺毛细血管网发育不全为主要原因，临床呈隐匿性进展，典型表现为劳力性呼吸困难、发绀及杵状指（趾）。血管造影和多层螺旋CT血管成像是主要的诊断方法。现重点介绍该病近年来的研究进展。Congenital pulmonary arteriovenous fistula is a clinical rare abnormality of pulmonary vessels. The main reason is pulmonary capillary network hypoplasia. The clinical disease progression is occult. Exertional dyspnea, cyanosis and acropachy are the classical phenotypes. The key diagnosis methods include angiogram and multi - slice spiral CT angiography. The research progress of this disease was reviewed in this paper.

关 键 词：先天性肺动静脉瘘 诊断 治疗 

分 类 号：R725.4[医药卫生—儿科]