儿童肾囊性疾病的诊治  

Diagnosis and treatment of cystic kidney disease in children

作　　者：姚俊 夏正坤 Yao Jun Xia Zhengkun(Department of Pediatrics, Nanjing General Hospital, Nanjing 210002, China)

机构地区：[1]南京总医院儿科,210002

出　　处：《国际儿科学杂志》2017年第1期40-43,51,共5页International Journal of Pediatrics

基　　金：国家自然科学基金（81270800）

摘　　要：PoRer分型将儿童肾囊性疾病分为4型：常染色体隐性遗传性多囊性肾病、多囊性肾发育不良、常染色体显性遗传性多囊性肾病、梗阻性囊性发育不良肾。此外，单纯性肾囊肿、发生在肾肿瘤及其他伴囊性肾病的综合征也可引起肾脏呈囊性改变。这类病由于其发病机制和病理基础不同，临床诊断及治疗方案选择亦不同，要正确诊断这类疾病，需要仔细分类并查明病因。该文就儿童常见的肾囊性疾病进行综述。There are four type of Potter typing of cystic kidney disease in children： autosomal recessive polycystic kidney disease, multicystic dysplastic kidney, autosomal dominant polycystic kidney disease and obstructive cystic dysplastic kidney. However, simple cyst of kidney multilocular cystic renal tumors and other genetic syndrome also can make kidney cystic change. Due to the different pathogenesis and pathological basis, the clinical diagnosis and treatment is also different. The correct diagnosis of these diseases requires chinical classification and determination of the causes of the diseases. This paper will make a review on the common cystic kid- ney disease in children.

关 键 词：肾囊性疾病 儿童 

分 类 号：R726.9[医药卫生—儿科]