婴幼儿孤立性先天性主动脉缩窄35例临床分析  

Clinical analysis of isolated coarctation of aorta in infants and toddlers

作　　者：肖燕燕[1] 金梅[1] 丁文虹[1] 王霄芳[1] 梁永梅[1] 吕震宇[1] 韩玲[1] 

机构地区：[1]首都医科大学附属北京安贞医院-北京市心肺血管疾病研究所小儿心脏科,100029

出　　处：《心肺血管病杂志》2017年第1期27-29,共3页Journal of Cardiovascular and Pulmonary Diseases

摘　　要：目的:探讨婴幼儿孤立性先天性主动脉缩窄的临床表现及其诊断治疗。方法:回顾性分析2011年1月1日至2015年12月31日期间收治的孤立性先天性婴幼儿(≤3岁)主动脉缩窄患者,总结其临床表现、治疗、随诊情况等。结果:经超声或CT、导管造影检查明确诊断,单纯婴幼儿先天性主动脉缩窄患者35例,男女比例21/14。临床心功能Ⅱ级31例,Ⅲ级2例,Ⅳ级2例。一期手术根治31例,未手术4例,死亡0例,术后复查超声心动图心功能均获一定改善。结论:先天性孤立性主动脉缩窄是严重影响婴幼儿左心功能的心脏疾病,早期诊断早期治疗可获得良好效果,手术后仍需长时间药物治疗,改善心功能。Objective： To discuss the clinical manifestation and diagnosis and therapy of the isolated coarctation of aorta（CoA） in infants and toddlers. Methods：to retrospective analysis the CoA patients whose age was ≤3 yrs and hospitalized from Jan, 2011 to Dec,2015, summarize the clinical manifestation, therapy and follow up. Results：35 cases were determined the diagnosis by echocardiography and/or CT. Male patients 21and female patients14. NYHA heart function grade Ⅱ 31cases,grade Ⅲ2 cases and gradeiV 2 cases. 31cases had surgery procedure and 4 cases had not, no death. Follow up echocardiography reveal the significant improvement of the heart dysfuntion. Conlclusion： Isolated CoA can lead to severe injury of heart function in infants and toddlers, early diagnosis and therapy can have good effects. Long term medicine should be used to promote heart function.

关 键 词：婴幼儿 孤立性 主动脉缩窄 

分 类 号：R54[医药卫生—心血管疾病]