先天性心脏病相关肺动脉高压诊断与治疗的研究进展  

Research progress on diagnosis and treatment of congenital heart disease associated pulmonary hypertension

作　　者：乔飞[1] 刘迎龙[1] 

机构地区：[1]首都医科大学附属北京安贞医院小儿心脏中心,100029

出　　处：《中国医药》2017年第6期938-941,共4页China Medicine

基　　金：国家自然科学基金（81570443）

摘　　要：肺动脉高压是小儿先天性心脏病常见的并发症，如不及时诊断和治疗，会影响到先天性心脏病患儿的根治效果，直接或者间接地影响患儿的生活质量。先天性心脏病相关肺动脉高压的及时诊断与治疗，选择适当的手术方式与时机，指导围术期管理，对缓解先天性心脏病患儿的症状，提高其生存质量，具有重要意义。本文就肺动脉高压的基本概念、病理生理特点、辅助检查、药物治疗、手术治疗方法进行综述，为先天性心脏病并发肺动脉高压患儿的进一步研究提供依据。Pulmonary arterial hypertension （PAH） is a common complication of congenital heart disease （CHD） , with significantly adverse effects on curative effect and quality of life in children with CHD without timely diagnosis and treatment. Study on diagnosis and treatment of CHD-associated PAH helps make decisions for surgical tinting, procedures and perioperative management, which can alleviate symptoms and improving life quality in children with CHD. This paper reviewed basic concepts, pathophysiological features, auxiliary examinations, drug therapies and surgical treatments of PAH, to provide references for studies on CHD-associated PAH.

关 键 词：先天性心脏病 高血压 肺性 诊断 治疗学 

分 类 号：R541[医药卫生—心血管疾病]