小儿中枢神经系统非典型畸胎瘤样/横纹肌样瘤的影像表现  

Imaging findings of atypical teratoid/rhabdoid tumor of central nervous system with clinical correlation

作　　者：戴望春 刘鸿圣 陈希文 曾斯慧 吴倩倩 陈元凯 刘振清 

机构地区：[1]广州市妇女儿童医疗中心放射科,510623

出　　处：《中华放射学杂志》2017年第8期612-615,共4页Chinese Journal of Radiology

基　　金：广东省科学技术厅科技计划项目（2016ZC0227）

摘　　要：目的 探讨小儿中枢神经系统（CNS）非典型畸胎瘤样/横纹肌样瘤（AT/RT）的影像特点.方法 回顾性分析2011年1月至2016年8月9例经病理证实的AT/RT的临床、影像资料,结合相关文献进行复习.本组男5例、女4例;年龄0.6~5.0岁,中位年龄1.4岁.9例均行MR平扫及增强检查,1例行CT平扫及增强扫描.结果 9例患儿肿瘤最大径4.8~7.8 cm,8例肿瘤位于脑内、1例位于腰骶段脊髓内;9例肿瘤均合并坏死,囊变8例,出血5例.DWI上呈不均匀高信号,ADC为低信号.2例病灶侵犯脑膜,2例脑脊液播散,1例发生脑转移.结论 CNS原发性AT/RT的影像表现有一定特异性,有助于诊断.Objective To evaluate the imaging characteristics of atypical teratoid/rhab doid tumor （AT/RT） of central nervous system（CNS）, and to improve the diagnostic ability of the disease. Methods The clinical and imaging findings of 9 patients were retrospectively analyzed. There were 5 male and 4 female, ages 7 months to 5 years,median age was 1.4 years. MR enhancement studies were obtained in all the cases. One case had CT enhancement examination. Results The lesions were seen in brain in 8 cases and in lumbosacral spinal cord in one case. The tumors size varied from 4.8—7.8 cm, Necrosis was seen in nine cases, cystic change in eight cases and hemorrhage in five cases. The tumors had high signal on DWI, and low signal on ADC map. Dura matter invasion（2 cases）, cerebrospinal fluid spread（2 cases）and intracerebral metastasis were seen. Conclusion There are some relatively specific imaging findings of primary CNS AT/RT that could assist their diagnosis.

关 键 词：非典型畸胎瘤样/横纹肌样瘤 磁共振成像 儿童 

分 类 号：R445.2[医药卫生—影像医学与核医学] R739.4[医药卫生—诊断学]