永存原始玻璃体增生症的临床特征及超声诊断价值  

Clinical Characteristics and Value of Ultrasonography in Diagnosis of Persistent Hyperplastic Primary Vitreous

作　　者：郑建美 林新霖[1] 魏巍丽 

机构地区：[1]福建医科大学附属第一医院干部病房科,福建福州350001 [2]福建医科大学附属第一医院超声科,福建福州350001

出　　处：《中外医疗》2017年第26期188-189,192,共3页China & Foreign Medical Treatment

摘　　要：目的探讨永存原始玻璃体增生症(persistent hyperplastic primary vitreous,PHPV)的临床特征及超声表现,以提高对该病的进一步认识和鉴别能力。方法回顾性分析2009年1月—2016年12月间9例该院临床确诊的PHPV临床表现及超声特征。结果 9例(10眼)PHPV在超声上均表现为玻璃体内出现圆锥形或漏斗状高回声团块,从晶状体后连接至视乳头,CDFI示其内可见条状血流信号,PW测及形态与视网膜中央动脉相似的频谱;所有患眼眼球缩小、眼轴缩短,与健侧比较差异有统计学意义(P<0.05);7例(8眼)患眼晶状体异常,并发白内障,2例患眼晶状体向前突出,前房浅。结论 PHPV的超声表现具有特征性,超声可显示玻璃体内增生组织的形态,对PHPV的诊断和鉴别诊断有重要参考价值。Objective This p a p e r tr ies to s tudy th e c l in ic a l c h a ra c te r is t ic s an d ultrason og raph y diagnosis of p e rs is te n t hy-perplast ic primary vitreous and to improve the identificat ion abil ity. Methods From Jan u a ry 2 00 9 to Dec emb er 2 01 6 C lini-cal features and ul trasonographic features of 9 cases were retrospectively analyzed. Results In th e 9 c a se s （10 eyes） with PHPV in the ultrasound diagnos is , a conical or funnel - shaped hyperechoic mass from the lens to optic papi l la in vitreous e-cho free zone was detected, and CDFI showed strip blood flow signals. PW and the shape of the ret ina with the central ar tery was similar to the spectrum; al l suffering from eyeballs narrowing, axial shor tening,compared with the contralateral , the difference was s tat is t ical ly signif icant （P〈0.05） ; 7 cases （8 eyes） had the abnormal lens in the eyeball of affected side, complicated by cataract ; 2 cases had abnormal lens and the anterior chamber was shallow. Conclusion PH PV shows c h a r -acter ist ic manifestat ions on ultrasound images, which is helpful in different ial diagnosis and guiding treatment plan.

关 键 词：永存原始玻璃体增生症 超声诊断 白瞳症 

分 类 号：R445[医药卫生—影像医学与核医学]