胡桃夹综合征诊断治疗进展——基于英国胡桃夹综合征指南  

Advances in diagnosis and treatment of Nutcracker syndrome--Based on the guideline of Nutcracker syndrome in England

作　　者：管娜[1] 

机构地区：[1]北京大学第一医院儿科,100034

出　　处：《中华实用儿科临床杂志》2017年第23期1773-1776,共4页Chinese Journal of Applied Clinical Pediatrics

摘　　要：胡桃夹综合征临床表现轻重不一，常见表现为非肾小球性血尿和直立性蛋白尿，此外还可表现为直立不耐受、腹痛、腰痛、胃肠道症状和性腺静脉曲张等，严重者可导致失血性贫血和肾静脉血栓。对于不典型表现者易被误诊和漏诊。75%的患儿经24个月保守治疗可恢复。一些直立调节障碍者应用米多君和肾上腺皮质激素治疗有效。对于病情严重者需手术干预。2017年英国发表了胡桃夹综合征诊治指南，现结合该指南介绍相关诊治进展。Patients with Nutcracker syndrome manifest with different symptoms, and microscopic non-glomerular hematuria, orthostatic proteinuria are the common features, and orthostatic intolerance, abdominal or flank pain, gastrointestinal symptoms and gonadal varices, etc.are also can be seen.Severe syndromes can lead to hemorrhagic anemia and renal thrombosis.Patients with uncommon symptoms might be misdiagnosed or missed diagnosis.Around 75% of children with Nutcracker syndrome will relieve after 24 months conservative therapy.Some patients with orthostatic adjustment disorder can be effectively treated by midodrine and cortin, however, some children with severe symptoms need surgical treatment.Now, the progress on diagnosis and treatment of Nutcracker syndrome based on guideline published by England in 2017 is introduced.

关 键 词：胡桃夹综合征 诊断 治疗 

分 类 号：R726.9[医药卫生—儿科]