血管瘤并血小板减少综合征介入栓塞治疗的效果分析  

Interventional treatment for Kasabach-Merrit syndrome in children:a report of 7 cases

作　　者：黄文雅[1] 肖天[1] 李春旺[1] 邓敏[1] 金科[1] 

机构地区：[1]湖南省儿童医院放射科,湖南省长沙市410007

出　　处：《临床小儿外科杂志》2018年第1期43-46,共4页Journal of Clinical Pediatric Surgery

摘　　要：目的分析血管瘤并血小板减少综合征经介入栓塞治疗的效果。方法收集2011年12月至2015年12月间本院收治的7例KM综合征患儿作为研究对象,所用病例在DSA透视下进行选择性动脉栓塞治疗。结果 7例患者中,颌面部1例,躯干3例,肩部2例,颈部1例。血小板均在60×10~9/L以下,最少7×10~9/L。治愈4例,好转3例,无死亡病例,介入治疗效果良好。结论血管瘤并血小板减少综合征患儿如果能早期选择介入治疗,多数病例预后较好,但无法根除原发灶的广泛性血管畸形。介入手术治疗对颌面部、颈部、躯干部位的KM综合征疗效确切,副反应小,值得推广。Objective To evaluate the clinical outcomes of Kasabach-Merrit syndrome and examine its interventional treatments. Methods This retrospective study was conducted for 7 patients with Kasabach-Mer- rit syndrome receiving selective arterial embolization by DSA （digital subtraction angiography）. Results The sites included maxillofacial region （ n = 1 ） , trunk （ n = 3 ） , shoulder （ n = 2 ） and neck （ n =1 ）. The count of platelet 7 × 109/L to 60 × 109/L. The outcomes were cure （ n =4） and improvement （n = 3）. Conclusion At an early stage,this disease may be treated interventionally with an excellent prognosis. However, generalized primary vascular malformations are not eradicated in most cases. The prognosis is poor for combined platelet reduction. In- terventional surgery of jaw-face ,neck and trunk area of KM syndrome is effective and have few side effects. It is worthy of wider promotion.

关 键 词：血管瘤 血小板减少 综合征 介入治疗 

分 类 号：R725.5[医药卫生—儿科] R732.2[医药卫生—临床医学]