具有自身免疫特征的间质性肺炎的特点  

Characteristics of interstitial pneumonia with autoimmune features

作　　者：陈健聪 吴锡平[2] 

机构地区：[1]南方医科大学第二临床医学院临床医学系,广州510280 [2]南方医科大学珠江医院呼吸内科,广州510280

出　　处：《国际呼吸杂志》2018年第4期306-310,共5页International Journal of Respiration

摘　　要：特发性间质性肺炎是一类以肺部出现弥漫性炎症和/或纤维化为特征的疾病。临床上,部分特发性间质性肺炎患者具有自身免疫特征,但是尚不能确诊为某一特定的结缔组织病。2015年,欧洲呼吸病学会和美国胸科学会建议将其命名为“具有自身免疫特征的间质性肺炎（IPAF）”。IPAF与其他间质性肺疾病相似,但是其在流行病学、临床表现、血清学检查、形态学表现、肺功能检查、其他检查以及预后方面均具有一定的特点。为了便于临床及早正确诊断和治疗IPAF,现将其特点及其与其他间质性肺疾病的比较进行综述。The idiopathic interstitial pneumonia is a kind of diseases characterized by diffuse inflammatory and/or fibrosis of lung. Clinically, some patients with idiopathic interstitial pneumonia have autoimmune features, but still don~ t meet established criteria for a connective tissue disease. In 2015, European Respiratory Society/American Thoraic Society proposed the term ＂interstitial pneumonia with autoimmune features （IPAF）＂. IPAF is similar to other interstitial lung diseases, but it has some characteristics in epidemiology, clinical manifestation, serological test, morphological features, lung function test, other examinations, and prognosis. In order to improve the timely diagnosis and treatment, its characteristics and comparisons with other interstitial lung diseases are reviewed.

关 键 词：具有自身免疫特征的间质性肺炎 间质性肺疾病 特点 比较 

分 类 号：R563.13[医药卫生—呼吸系统]