左心发育不良综合征一例及国内治疗现状  

One case report of hypoplasitc left heart syndrome and domestic status

作　　者：张泽伟[1] 高强[1] 高展 林茹[1] 吴秀静[1] 马良龙[1] 齐建川[1] 施旭聪 

机构地区：[1]浙江大学医学院附属儿童医院心脏外科,杭州310000

出　　处：《中华小儿外科杂志》2018年第2期112-115,共4页Chinese Journal of Pediatric Surgery

基　　金：浙江省公益技术研究项目（2014C33G2010234）

摘　　要：目的通过我院1例左心发育不全综合征治疗的成功案列，探讨左心发育不全综合征的外科治疗。方法检索国内外外科治疗左心发育不全综合征的相关文献，结合我院病例，阐述国内左心发育不全综合征治疗现状，对左心发育不全综合征的外科治疗进行详细总结。结果我院1例左心发育不全综合征患儿在行Norwood I期＋ Sano术后顺利恢复出院。临床经验及文献检索都表明我国仅少数医院成功实施了Norwood手术，术后维持体-肺循环的动态平衡是患儿存活的关键。结论我国对左心发育不全综合征的外科治疗仍处于起步阶段，Norwood手术是治疗左心发育不全综合征的有效方法，维持体-肺循环的动态平衡是患儿存活的关键。ObjectiveTo summarize the surgical experience of hypoplastic left heart syndrome （HLHS）.MethodsBased on clinical profiles and databases, current domestic status was discussed for surgical treatment of HLHS.ResultsOne child with HLHS was successfully operated at our hospital. Clinical experiences and literature searches shown that only few domestic hospitals had successfully implemented Norwood surgery. Postoperative maintenance of body-pulmonary vascular balance is essential for survival.ConclusionsSurgical treatment of HLHS is still elementary in China. Norwood surgery is an effective treatment for HLHS and maintaining a dynamic balance of body-pulmonary circulation is vital.

关 键 词：左心发育不全综合征 Norwood手术 肺循环 

分 类 号：R726.5[医药卫生—儿科]