法洛四联症根治术后中远期常见并发症及治疗  

The Long-term Common Complications and Its Treatments after Tetralogy of Fallot Repair

作　　者：王官玺 何凤璞 李守军[1] WANG Guan-xi;HE Feng-pu;LI Shou-jun.(Pediatric Cardiac Surgery Center, Fuwai Hospital, National Center for Cardiovascular Disease, Chinese Academy of Medical Sciences, Peking Union Medical College, Beijing, 100037 China.)

机构地区：[1]北京协和医学院中国医学科学院国家心血管病中心阜外医院小儿外科中心,北京市100037

出　　处：《中国分子心脏病学杂志》2018年第2期2453-2456,共4页Molecular Cardiology of China

基　　金：首都临床特色应用研究(Z141107002514002)

摘　　要：法洛四联症是最常见的复杂先天性心脏病,根治手术效果良好,30年远期生存率约90%。然而根治术后中远期可能会出现一些并发症,包括:肺动脉瓣反流、三尖瓣反流、主动脉根部扩张、心力衰竭、心律失常和猝死等,会不同程度的影响术后远期预后及生活质量。因此,法洛四联症患者术后需要进行长期的随访和管理,在合适的时机对这些并发症进行治疗,以期延长患者的生存时间,提高生存质量。Tetralogy of Fallot is the most common complex congenital heart disease, and the surgical outcome is excellent with the 30 years survival rate coming to 90%. However, many patients require reintervention in adulthood for its, complications, including pulmonary valve regurgitation, tricuspid valve regurgitation, aortic root dilation, heart failure, arrhythmia and sudden death, which affect the long-term prognosis and quality of life. As a result, patients with tetralogy of Fallot need long-term follow-up and management, and it＇s vital to treat the associated complications at the right time, thus prolonging the survival time and improving the quality of life.

关 键 词：先天性心脏病 法洛四联症 肺动脉瓣返流 主动脉根部扩张 心律失常 

分 类 号：R654.2[医药卫生—外科学]