胸廓窒息性发育不良影像表现(双胞胎病例报告及文献复习)  

Asphyxiating Thoracic Dysplasia:A Report of two Cases Report and a Review of the Literature

作　　者：张骥[1] 缪红[1] 顾莱莱[1] 

机构地区：[1]上海市儿童医院放射科,上海200041

出　　处：《实用放射学杂志》2002年第9期801-803,共3页Journal of Practical Radiology

摘　　要：目的　提高对胸廓窒息性发育不良影像及临床表现的认识。方法　报告 2例胸廓窒息性发育不良患儿X线和CT影像改变 ,并结合临床表现和有关文献加以讨论。结果　胸廓窒息性发育不良主要X线表现为 :(1)胸片和CT示肋骨短、肋骨头膨大、胸部前后径较窄 ;(2 )髂翼呈方形 ,髋臼水平位 ,股骨头骨骺骨化提前 ;(3 )临床常表现为反复呼吸道感染。结论　该病相当少见 ,对反复肺部感染的患儿 ,应警惕该病存在可能 ,X检查可给以明确的结论。Objective To improve X-ray and clinical knowledge of asphyxiating thoracic dysplasia(ATD).Methods X-ray film and CT findings of twin infants were studied meanwhile relative literature about ATD was reviewed.Results The main positive fingings of ATD were as follow:(1)The thoracic cages were both shorter than usual in the transverse and anterioposterior diameter;the anterior ends of the ribs are widened and cupped;(2)The pelvis also show abnormalities which include some flaring of the ilia,and early ossification of the centers for the capital femoral epiphyses;(3)Incureable respiratory infection was the prominent clinical manifestation.Conclusion ATD,a rarely seen disease,often occurs in those patients who suffer from pneumonia repeatedly;Because plain films can clearly show the relative characteristic deformity changes of thoracic cage and pelvis,X-ray examination can be regarded as the most important diagnostic method.

关 键 词：胸廓窒息性发育不良 临床表现 影像学表现 X线 诊断 CT诊断 ATD 

分 类 号：R681.1[医药卫生—骨科学] R596[医药卫生—外科学]