结缔组织病合并特发性门静脉高压症1例  

One case of connective tissue disease complicated with idiopathic portal hypertension

作　　者：胡秋[1] 黄勤[1] 刘冬舟[1] HU Qiu;HUANG Qin;LIU Dong-zhou(Rheumatology and Immunology Department,Shenzhen People's Hospital,2nd Clinical Medical College of Ji'nan University,Shenzhen 518001,China)

机构地区：[1]暨南大学第二临床医学院附属深圳市人民医院风湿免疫科,广东深圳518001

出　　处：《临床医学研究与实践》2018年第8期10-11,共2页Clinical Research and Practice

摘　　要：目的探讨结缔组织病合并特发性门静脉高压症(IPH)的临床特征、诊断及其治疗方法。方法回顾性分析我院确诊的1例结缔组织病合并IPH患者的临床特点,随访观察治疗结果并结合文献报道进行总结分析。结果患者在病程中出现呕血、黑便、脾亢进等门脉高压表现,血液系统三系降低,抗核抗体、抗SSA抗体、抗SSB抗体阳性。经降低门脉压力以及控制结缔组织病治疗后好转。结论结缔组织病合并IPH发病率较低、发病机制不明,相关病例报道非常罕见,常造成临床上的误诊或漏诊,故结缔组织病患者出现门脉高压时应警惕IPH,以免延误治疗。Objective To explore the clinical features,diagnosis and treatment of connective tissue disease with idiopathic portal hypertension(IHP).Methods The clinical characteristics of 1 cases of connective tissue disease with IHP diagnosed in our hospital were analyzed.The treatment results were followed up and observed,and the combined literature were summed up and analyzed.Results The main symptoms were hematemesis,melena,hypersplenism and portal hypertension,the three lines decreased of blood system,antinuclear antibody,anti SSA antibody and anti SSB antibody positive anticardiolipin antibody.After reducing portal pressure and controlling connective tissue disease,it improved.Conclusion Connective tissue disease combined with IHP has a low incidence and unclear pathogenesis.The related case reports are rare,and often resulting in clinical misdiagnosis or missed diagnosis.In order to avoid delays in treatment,we report this case to indicate the clinicians not to ignore connective tissue disease with IPH

关 键 词：结缔组织病 特发性门静脉高压症(IPH) 诊断 

分 类 号：R593.2[医药卫生—内科学]